ORPHA:439737
Primary polyarteritis nodosa
Synonyms: Primary PAN · Primary periarteritis nodosa
- Type
- Clinical subtype
- Group
- Subtype of disorder
- Inheritance
- Not applicable
- Status
- active
Orphadata ships no English definition for this code.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Primary polyarteritis nodosa | Primary PAN · Primary periarteritis nodosa |
| fr | Périartérite noueuse primaire | PAN primaire · Polyartérite noueuse primaire |
| de | Primäre Polyarteriitis nodosa | Periarteriitis nodosa, primäre · Primäre PAN |
| es | Poliarteritis nodosa primaria | PAN primaria · Periarteritis nodosa primaria |
| it | Poliarterite nodosa primitiva | PAN primitiva · Periarterire nodosa primitiva |
| nl | Primaire polyarteriitis nodosa | Primaire periarteriitis nodosa · Primaire PAN |
| pt | Poliarterite nodosa primária | |
| pl | Pierwotne guzkowe zapalenie tętnic | Pierwotne PAN |
| cs | Primární polyarteritis nodosa | Primární PAN · Primární periarteritis nodosa |
| uk | Первинний вузликовий поліартеріїт | Первинний PAN · Первинний вузликовий периартеріїт |
| zh | 原发性结节性多动脉炎 | 原发性结节性动脉周围炎 |
| tr | Primer poliarteritis nodoza | Primer PAN · Primer periarterit nodosa |
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | M30.0 | NTBT | attributed | validated |
| ICD-11 | 4A44.4 | NTBT | attributed | validated |
| MONDO | 0018593 | E | validated | |
| UMLS | C5680052 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:767Polyarteritis nodosa
rare neurological diseases; rare renal diseases; rare systemic and rheumatological diseases; rare circulatory system diseases; rare systemic or rheumatologic diseases of childhood; rare transplant-related disorders
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Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
0 recordsNo prevalence record in this release.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/439737
- This record as JSON: /data/d/439737.json