raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:439737

Primary polyarteritis nodosa

Synonyms: Primary PAN · Primary periarteritis nodosa

Type
Clinical subtype
Group
Subtype of disorder
Inheritance
Not applicable
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enPrimary polyarteritis nodosaPrimary PAN · Primary periarteritis nodosa
frPériartérite noueuse primairePAN primaire · Polyartérite noueuse primaire
dePrimäre Polyarteriitis nodosaPeriarteriitis nodosa, primäre · Primäre PAN
esPoliarteritis nodosa primariaPAN primaria · Periarteritis nodosa primaria
itPoliarterite nodosa primitivaPAN primitiva · Periarterire nodosa primitiva
nlPrimaire polyarteriitis nodosaPrimaire periarteriitis nodosa · Primaire PAN
ptPoliarterite nodosa primária
plPierwotne guzkowe zapalenie tętnicPierwotne PAN
csPrimární polyarteritis nodosaPrimární PAN · Primární periarteritis nodosa
ukПервинний вузликовий поліартеріїтПервинний PAN · Первинний вузликовий периартеріїт
zh原发性结节性多动脉炎原发性结节性动脉周围炎
trPrimer poliarteritis nodozaPrimer PAN · Primer periarterit nodosa
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10M30.0NTBTattributedvalidated
ICD-114A44.4NTBTattributedvalidated
MONDO0018593Evalidated
UMLSC5680052Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

  • ORPHA:767Polyarteritis nodosa
    rare neurological diseases; rare renal diseases; rare systemic and rheumatological diseases; rare circulatory system diseases; rare systemic or rheumatologic diseases of childhood; rare transplant-related disorders

Children (3):

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card