Single-organ polyarteritis nodosa
Synonyms: Single-organ PAN · Single-organ periarteritis nodosa
- Type
- Clinical subtype
- Group
- Subtype of disorder
- Inheritance
- Not applicable
- Status
- active
Single-organ polyarteritis nodosa (PAN) is a rare, often mild form of PAN characterized by limited disease without generalized manifestations, most often affecting the skin (cutaneous PAN), the brain, eyes, pancreas, testicles, ureter, breasts, or ovaries. Affected patients are often younger than those with systemic PAN and relapses appear to be more common.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Single-organ polyarteritis nodosa | Single-organ PAN · Single-organ periarteritis nodosa |
| fr | Périartérite noueuse à organe unique | PAN à organe unique · Polyartérite noueuse à organe unique |
| de | Isolierte Organvaskulitis vom Typ der Polyarteriitis nodosa | Einzelorgan-PAN · Periarteriitis nodosa, isoliertes Organ |
| es | Poliarteritis nodosa de órgano único | PAN de órgano único · Periarteritis nodosa de órgano único |
| it | Poliarterite nodosa di un solo organo | PAN di un solo organo · Periarterite nodosa di un solo organo |
| nl | Polyarteriitis nodosa van een enkel orgaan | PAN van een enkel orgaan · Periarteriitis nodosa van een enkel orgaan |
| pt | Poliarterite nodosa, orgão - único | |
| pl | Guzkowe zapalenie tętnic jednego narządu | PAN w obrębie jednego narządu |
| cs | Jednoorgánová polyarteritis nodosa | Jednoorgánová PAN · Jednoorgánová periarteritis nodosa |
| uk | Одноорганний вузликовий поліартеріїт | Одноорганний PAN · Одноорганний вузликовий періартеріїт |
| zh | 单器官结节性多动脉炎 | 单器官结节性动脉周围炎 |
| tr | Tek organlı poliarteritis nodoza | Tek organlı PAN · Tek organlı periarterit nodosa |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | M30.0 | NTBT | attributed | validated |
| ICD-11 | 4A44.4 | NTBT | attributed | validated |
| MONDO | 0018595 | E | validated | |
| UMLS | C5680051 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:439737Primary polyarteritis nodosa
rare neurological diseases; rare renal diseases; rare systemic and rheumatological diseases; rare circulatory system diseases; rare systemic or rheumatologic diseases of childhood; rare transplant-related disorders
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/439755
- This record as JSON: /data/d/439755.json