{"orpha":439737,"name":"Primary polyarteritis nodosa","type":"Clinical subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":["Primary PAN","Primary periarteritis nodosa"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-439737/","orphanet_url":"https://www.orpha.net/en/disease/detail/439737","names":{"fr":{"name":"Périartérite noueuse primaire","synonyms":["PAN primaire","Polyartérite noueuse primaire"]},"de":{"name":"Primäre Polyarteriitis nodosa","synonyms":["Periarteriitis nodosa, primäre","Primäre PAN"]},"es":{"name":"Poliarteritis nodosa primaria","synonyms":["PAN primaria","Periarteritis nodosa primaria"]},"it":{"name":"Poliarterite nodosa primitiva","synonyms":["PAN primitiva","Periarterire nodosa primitiva"]},"nl":{"name":"Primaire polyarteriitis nodosa","synonyms":["Primaire periarteriitis nodosa","Primaire PAN"]},"pt":{"name":"Poliarterite nodosa primária"},"pl":{"name":"Pierwotne guzkowe zapalenie tętnic","synonyms":["Pierwotne PAN"]},"cs":{"name":"Primární polyarteritis nodosa","synonyms":["Primární PAN","Primární periarteritis nodosa"]},"uk":{"name":"Первинний вузликовий поліартеріїт","synonyms":["Первинний PAN","Первинний вузликовий периартеріїт"]},"zh":{"name":"原发性结节性多动脉炎","synonyms":["原发性结节性动脉周围炎"]},"tr":{"name":"Primer poliarteritis nodoza","synonyms":["Primer PAN","Primer periarterit nodosa"]}},"xrefs":[{"source":"ICD-10","code":"M30.0","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"4A44.4","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"MONDO","code":"0018593","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5680052","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98023,"name":"Rare systemic or rheumatologic disease"},"parents":[{"orpha":767,"name":"Polyarteritis nodosa","classifications":[181,188,196,198,231,233]}],"children":[{"orpha":439729,"name":"Cutaneous polyarteritis nodosa","type":"Clinical subtype"},{"orpha":439755,"name":"Single-organ polyarteritis nodosa","type":"Clinical subtype"},{"orpha":439762,"name":"Systemic polyarteritis nodosa","type":"Clinical subtype"}],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":[],"prevalence":[],"phenotypes":null}