ORPHA:439729
Cutaneous polyarteritis nodosa
Synonyms: Cutaneous PAN · Cutaneous periarteritis nodosa
- Type
- Clinical subtype
- Group
- Subtype of disorder
- Inheritance
- Not applicable
- Status
- active
Cutaneous polyarteritis nodosa (CPAN) is a rare limited form of polyarteritis nodosa (PAN), characterized by cutaneous vasculitis and mild and transient extracutaneous manifestations such as mild arthralgia, arthritis,myalgia, and rarely peripheral neuropathy.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Cutaneous polyarteritis nodosa | Cutaneous PAN · Cutaneous periarteritis nodosa |
| fr | Périartérite noueuse cutanée | PAN cutanée · Polyartérite noueuse cutanée |
| de | Kutane Polyarteriitis nodosa | Kutane PAN · Kutane Periarteriitis nodosa |
| es | Poliarteritis nodosa cutánea | PAN cutánea · Periarteritis nodosa cutánea |
| it | Poliarterite nodosa cutanea | PAN cutanea · Periarterite nodosa cutanea |
| nl | Cutane polyarteriitis nodosa | Cutane PAN · Cutane periarteriitis nodosa |
| pt | Poliarterite nodosa cutânea | |
| pl | Skórne guzkowe zapalenie tętnic | Skórne PAN |
| cs | Kožní polyarteritis nodosa | Kožní PAN · Kožní periarteritis nodosa |
| uk | Вузликовий шкірний поліартеріїт | Шкірний PAN · Вузликовий шкірний періартеріїт |
| zh | 皮肤结节性多动脉炎 | 皮肤结节性动脉周围炎 |
| tr | Kutanöz poliarteritis nodoza | Kutanöz PAN · Kutanöz periarterit nodosa |
Definition in:
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | M30.0 | NTBT | attributed | validated |
| ICD-11 | EF40.Z | NTBT | index | validated |
| MONDO | 0018592 | E | validated | |
| UMLS | C0343190 | E | validated | |
| GARD | 7415 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:439737Primary polyarteritis nodosa
rare neurological diseases; rare renal diseases; rare systemic and rheumatological diseases; rare circulatory system diseases; rare systemic or rheumatologic diseases of childhood; rare transplant-related disorders
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
0 recordsNo prevalence record in this release.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/439729
- This record as JSON: /data/d/439729.json