ORPHA:439762
Systemic polyarteritis nodosa
Synonyms: Systemic PAN · Systemic periarteritis nodosa
- Type
- Clinical subtype
- Group
- Subtype of disorder
- Inheritance
- Not applicable
- Status
- active
Systemic polyarteritis nodosa (PAN) is a chronic systemic necrotizingvasculitis of adults and childrenaffecting small- and medium-sized vessels and characterized by formation of microaneurysms leading to serious generalized disease and multi-organ involvement.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Systemic polyarteritis nodosa | Systemic PAN · Systemic periarteritis nodosa |
| fr | Périartérite noueuse systémique | PAN systémique · Polyartérite noueuse systémique |
| de | Systemische Polyarteriitis nodosa | Periarteriitis nodosa, systemische · Systemische PAN |
| es | Poliarteritis nodosa sistémica | PAN sistémica · Periarteritis nodosa sistémica |
| it | Poliarterite nodosa sistemica | PAN sistemica · Periarterite nodosa sistemica |
| nl | Systemische polyarteriitis nodosa | Systemische PAN · Systemische periarteriitis nodosa |
| pt | Poliarterite nodosa sistémica | |
| pl | Układowe guzkowe zapalenie tętnic | Układowe PAN |
| cs | Systémová polyarteritis nodosa | Systémová PAN · Systémová periarteritis nodosa |
| uk | Системний вузликовий поліартеріїт | Системний PAN · Системний вузликовий периартеріїт |
| zh | 系统性结节性多动脉炎 | 系统性结节性血管周围炎 |
| tr | Sistemik poliarteritis nodoza | Sistemik PAN · Sistemik periarterit nodosa |
Definition in:
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | M30.0 | NTBT | attributed | validated |
| ICD-11 | 4A44.4 | NTBT | attributed | validated |
| MONDO | 0018596 | E | validated | |
| UMLS | C5848156 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:439737Primary polyarteritis nodosa
rare neurological diseases; rare renal diseases; rare systemic and rheumatological diseases; rare circulatory system diseases; rare systemic or rheumatologic diseases of childhood; rare transplant-related disorders
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
0 recordsNo prevalence record in this release.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/439762
- This record as JSON: /data/d/439762.json