ORPHA:3394
Soft tissue sarcoma
Synonyms: Malignant mesenchymal tumor · Malignant soft tissue tumor · Soft part sarcoma
- Type
- Clinical group
- Group
- Group of disorders
- Status
- active
This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Soft tissue sarcoma | Malignant mesenchymal tumor · Malignant soft tissue tumor · Soft part sarcoma |
| fr | Sarcome des tissus mous | Sarcome des parties molles · Tumeur maligne des parties molles · Tumeur maligne des tissus mous · Tumeur mésenchymateuse maligne |
| de | Weichteilsarkom | Mesenchymaler Tumor, maligner · Weichteiltumor, maligner |
| es | Sarcoma de partes blandas | Sarcoma de tejidos blandos · Tumor maligno de tejidos blandos · Tumor mesenquimal maligno |
| it | Sarcoma dei tessuti molli | Sarcoma delle parti molli · Tumore maligno dei tessuti molli · Tumore mesenchimale maligno |
| nl | Wekedelensarcoom | Kwaadaardige wekedelentumor · Maligne mesenchymale tumor · Maligne wekedelentumor |
| pt | Sarcoma de tecidos moles | Tumor mesenquimatoso maligno |
| pl | Mięsak tkanek miękkich | Złośliwy guz mezenchymalny · Złośliwy guz tkanek miękkich |
| cs | Sarkom měkkých tkání | Maligní mezenchymový nádor · Maligní nádor měkkých tkání |
| uk | Саркома мяких тканин | Злоякісна мезенхімальна пухлина · Злоякісна пухлина мяких тканин · Саркома мяких тканин |
| zh | 软组织肉瘤 | 恶性软组织肿瘤 |
| tr | Yumuşak doku sarkomu | Yumuşak bölüm sarkomu · Habis mezenkimal tümör · Habis yumuşak doku tümörü |
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| MONDO | 0018078 | E | validated | |
| MONDO | 18078 | E | validated | |
| GARD | 4898 | E | validated | |
| MedDRA | 10075333 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:71209Rare soft tissue tumor
rare neoplastic diseases
Children (26):
- ORPHA:163699Alveolar soft tissue sarcoma
- ORPHA:263413Angiosarcoma
- ORPHA:99966Atypical teratoid rhabdoid tumor
- ORPHA:31112Dermatofibrosarcoma protuberans
- ORPHA:83469Desmoplastic small round cell tumor
- ORPHA:293202Epithelioid sarcoma
- ORPHA:370334Extraskeletal Ewing sarcoma
- ORPHA:209916Extraskeletal myxoid chondrosarcoma
- ORPHA:2030Fibrosarcoma
- ORPHA:86902Follicular dendritic cell sarcoma
- ORPHA:590539Isolated melanotic schwannoma
- ORPHA:33276Kaposi sarcoma
- ORPHA:64720Leiomyosarcoma
- ORPHA:69078Liposarcoma
- ORPHA:730256Low-grade fibromyxoid sarcoma
- ORPHA:3148Malignant peripheral nerve sheath tumor
- ORPHA:79105Myxofibrosarcoma
- ORPHA:730892Ossifying fibromyxoid tumor
- ORPHA:370348Peripheral primitive neuroectodermal tumor
- ORPHA:69077Rhabdoid tumor
- ORPHA:780Rhabdomyosarcoma
- ORPHA:466962SMARCA4-deficient sarcoma of thorax
- ORPHA:730281Sclerosing epithelioid fibrosarcoma
- ORPHA:2126Solitary fibrous tumor
- ORPHA:3273Synovial sarcoma
- ORPHA:2023Undifferentiated pleomorphic sarcoma
4
Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
3 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | 1-9 / 100 000 | 3.6 / 100 000 | France | Value and class | Validated | 21826194[PMID] |
| Point prevalence | 1-5 / 10 000 | 30 / 100 000 | Europe | Value and class | Validated | European Medicines Agency 2015[OTHER] |
| Annual incidence | 1-9 / 100 000 | 4.74 / 100 000 | Europe | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/3394
- This record as JSON: /data/d/3394.json