raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:71209

Rare soft tissue tumor

Synonyms: Rare mesenchymal tumor

Type
Category
Group
Group of disorders
Status
active

This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enRare soft tissue tumorRare mesenchymal tumor
frTumeur rare des tissus mousTumeur mésenchymateurse rare · Tumeur rare des parties molles
deWeichteiltumor, seltener
esTumor raro de tejidos blandos
itTumore raro dei tessuti molli
nlZeldzame wekedelentumorZeldzame mesenchymale tumor
ptTumor raro dos tecidos moles
plRzadkie guzy tkanek miękkichRzadki guz mezenchymalny
csVzácný nádor měkkých tkáníVzácný mezenchymální nádor
ukРідкісна пухлина мяких тканинРідкісна мезенхімальна пухлина
zh罕见软组织肿瘤罕见间叶性肿瘤
trNadir yumuşak doku tümörüNadir mezenkimal tümör
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
MONDO19099Evalidated
UMLSC5680113Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

Children (15):

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card