{"orpha":3394,"name":"Soft tissue sarcoma","type":"Clinical group","group":"Group of disorders","status":"active","flags":[],"synonyms":["Malignant mesenchymal tumor","Malignant soft tissue tumor","Soft part sarcoma"],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-3394/","orphanet_url":"https://www.orpha.net/en/disease/detail/3394","names":{"fr":{"name":"Sarcome des tissus mous","synonyms":["Sarcome des parties molles","Tumeur maligne des parties molles","Tumeur maligne des tissus mous","Tumeur mésenchymateuse maligne"]},"de":{"name":"Weichteilsarkom","synonyms":["Mesenchymaler Tumor, maligner","Weichteiltumor, maligner"]},"es":{"name":"Sarcoma de partes blandas","synonyms":["Sarcoma de tejidos blandos","Tumor maligno de tejidos blandos","Tumor mesenquimal maligno"]},"it":{"name":"Sarcoma dei tessuti molli","synonyms":["Sarcoma delle parti molli","Tumore maligno dei tessuti molli","Tumore mesenchimale maligno"]},"nl":{"name":"Wekedelensarcoom","synonyms":["Kwaadaardige wekedelentumor","Maligne mesenchymale tumor","Maligne wekedelentumor"]},"pt":{"name":"Sarcoma de tecidos moles","synonyms":["Tumor mesenquimatoso maligno"]},"pl":{"name":"Mięsak tkanek miękkich","synonyms":["Złośliwy guz mezenchymalny","Złośliwy guz tkanek miękkich"]},"cs":{"name":"Sarkom měkkých tkání","synonyms":["Maligní mezenchymový nádor","Maligní nádor měkkých tkání"]},"uk":{"name":"Саркома мяких тканин","synonyms":["Злоякісна мезенхімальна пухлина","Злоякісна пухлина мяких тканин","Саркома мяких тканин"]},"zh":{"name":"软组织肉瘤","synonyms":["恶性软组织肿瘤"]},"tr":{"name":"Yumuşak doku sarkomu","synonyms":["Yumuşak bölüm sarkomu","Habis mezenkimal tümör","Habis yumuşak doku tümörü"]}},"xrefs":[{"source":"MONDO","code":"0018078","qualifier":"E","icd_relation":null,"validated":true},{"source":"MONDO","code":"18078","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"4898","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10075333","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":71209,"name":"Rare soft tissue tumor","classifications":[202]}],"children":[{"orpha":163699,"name":"Alveolar soft tissue sarcoma","type":"Disease"},{"orpha":263413,"name":"Angiosarcoma","type":"Disease"},{"orpha":99966,"name":"Atypical teratoid rhabdoid tumor","type":"Disease"},{"orpha":31112,"name":"Dermatofibrosarcoma protuberans","type":"Disease"},{"orpha":83469,"name":"Desmoplastic small round cell tumor","type":"Disease"},{"orpha":293202,"name":"Epithelioid sarcoma","type":"Disease"},{"orpha":370334,"name":"Extraskeletal Ewing sarcoma","type":"Disease"},{"orpha":209916,"name":"Extraskeletal myxoid chondrosarcoma","type":"Disease"},{"orpha":2030,"name":"Fibrosarcoma","type":"Disease"},{"orpha":86902,"name":"Follicular dendritic cell sarcoma","type":"Disease"},{"orpha":590539,"name":"Isolated melanotic schwannoma","type":"Disease"},{"orpha":33276,"name":"Kaposi sarcoma","type":"Disease"},{"orpha":64720,"name":"Leiomyosarcoma","type":"Disease"},{"orpha":69078,"name":"Liposarcoma","type":"Disease"},{"orpha":730256,"name":"Low-grade fibromyxoid sarcoma","type":"Disease"},{"orpha":3148,"name":"Malignant peripheral nerve sheath tumor","type":"Disease"},{"orpha":79105,"name":"Myxofibrosarcoma","type":"Disease"},{"orpha":730892,"name":"Ossifying fibromyxoid tumor","type":"Disease"},{"orpha":370348,"name":"Peripheral primitive neuroectodermal tumor","type":"Disease"},{"orpha":69077,"name":"Rhabdoid tumor","type":"Disease"},{"orpha":780,"name":"Rhabdomyosarcoma","type":"Disease"},{"orpha":466962,"name":"SMARCA4-deficient sarcoma of thorax","type":"Disease"},{"orpha":730281,"name":"Sclerosing epithelioid fibrosarcoma","type":"Disease"},{"orpha":2126,"name":"Solitary fibrous tumor","type":"Disease"},{"orpha":3273,"name":"Synovial sarcoma","type":"Disease"},{"orpha":2023,"name":"Undifferentiated pleomorphic sarcoma","type":"Disease"}],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[{"type":"Annual incidence","qualification":"Value and class","class":"1-9 / 100 000","value":3.6,"area":"France","status":"Validated","source":"21826194[PMID]"},{"type":"Point prevalence","qualification":"Value and class","class":"1-5 / 10 000","value":30.0,"area":"Europe","status":"Validated","source":"European Medicines Agency 2015[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"1-9 / 100 000","value":4.74,"area":"Europe","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"}],"phenotypes":null}