raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:99869

Thymic neuroendocrine carcinoma

Type
Disease
Group
Disorder
Inheritance
Not applicable
Age of onset
Adult
Status
active

Thymic neuroendocrine carcinoma is a type of thymic epithelial neoplasm displaying evidence of neuroendocrine differentiation.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enThymic neuroendocrine carcinoma
frCarcinome neuroendocrine thymiqueCNET
deThymuskarzinom, neuroendokrines
esCarcinoma neuroendocrino tímico
itCarcinoma neuroendocrino del timo
nlNeuro-endocrien thymuscarcinoom
ptTumor maligno do timo
plNeuroendokrynny rak grasicy
csNeuroendokrinní karcinom thymu
ukНейроендокринна карцинома тимуса
zh胸腺神经内分泌癌
trTimik nöroendokrin karsinom

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10C37NTBTattributedvalidated
ICD-112C27.1Especificvalidated
MONDO0020516Evalidated
UMLSC2210965Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (2):

Children (3):

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

1 record
TypeClassValueAreaQualificationValidationSource
Point prevalenceUnknown—WorldwideClass onlyValidatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card