raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:263339

Poorly differentiated thymic neuroendocrine carcinoma

Type
Histopathological subtype
Group
Subtype of disorder
Inheritance
Not applicable
Age of onset
Adult
Status
active

This disease is described under Thymic neuroendocrine carcinoma

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enPoorly differentiated thymic neuroendocrine carcinoma
frCarcinome neuroendocrine thymique peu différenciéCNET peu différencié
deThymuskarzinom, neuroendokrines, undifferenziert
esCarcinoma neuroendocrino tímico pobremente diferenciado
itCarcinoma neuroendocrino timico scarsamente differenziato
nlSlecht gedifferentieerd neuro-endocrien thymuscarcinoom
ptCarcinoma tímico neuroendócrino com reduzida diferenciação
plSłabo zróżnicowany rak neuroendokrynny grasicy
csMálo diferencovaný neuroendokrinní karcinom thymu
ukПогано диференційована нейроендокринна карцинома тимуса
zh低分化胸腺神经内分泌癌
trKötü diferansiye timik nöroendokrin karsinom
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10C37NTBTattributedvalidated
ICD-112C27.1NTBTindexvalidated
MONDO0016978Evalidated
UMLSC4305466Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

1 record
TypeClassValueAreaQualificationValidationSource
Point prevalenceUnknown—WorldwideClass onlyNot yet validatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card