{"orpha":99869,"name":"Thymic neuroendocrine carcinoma","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":[],"definition":"Thymic neuroendocrine carcinoma is a type of thymic epithelial neoplasm displaying evidence of neuroendocrine differentiation.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-99869/","orphanet_url":"https://www.orpha.net/en/disease/detail/99869","names":{"fr":{"name":"Carcinome neuroendocrine thymique","synonyms":["CNET"],"definition":"Le carcinome neuroendocrine thymique est un type de néoplasie épithéliale thymique exprimant une différentiation neuro-endocrine."},"de":{"name":"Thymuskarzinom, neuroendokrines","definition":"Das Neuroendokrine Thymuskarzinom, eine Form der malignen Thymusneoplasmen, zeigt Merkmale einer neuroendokrinen Differenzierung."},"es":{"name":"Carcinoma neuroendocrino tímico","definition":"El carcinoma neuroendocrino tímico es un tipo de neoplasia maligna de timo que muestra evidencias de diferenciación neuroendocrina."},"it":{"name":"Carcinoma neuroendocrino del timo"},"nl":{"name":"Neuro-endocrien thymuscarcinoom","definition":"Neuro-endocrien thymuscarcinoom (TC), een type kwaadaardig neoplasma van de thymus, vertoont kenmerken van neuro-endocriene differentiatie."},"pt":{"name":"Tumor maligno do timo","definition":"O carcinoma neuroendócrino tímico é um tipo de neoplasia maligna do timo exibindo evidência de diferenciação neuroendócrina."},"pl":{"name":"Neuroendokrynny rak grasicy"},"cs":{"name":"Neuroendokrinní karcinom thymu"},"uk":{"name":"Нейроендокринна карцинома тимуса","definition":"Thymic neuroendocrine carcinoma is a type of thymic epithelial neoplasm (see this term) displaying evidence of neuroendocrine differentiation."},"zh":{"name":"胸腺神经内分泌癌","definition":"胸腺神经内分泌癌是一种胸腺上皮肿瘤，表现为神经内分泌分化。"},"tr":{"name":"Timik nöroendokrin karsinom"}},"xrefs":[{"source":"ICD-10","code":"C37","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"2C27.1","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"381956131"},{"source":"MONDO","code":"0020516","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C2210965","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":100101,"name":"Neuroendocrine tumor with other location","classifications":[193,202]},{"orpha":3398,"name":"Thymic epithelial neoplasm","classifications":[202]}],"children":[{"orpha":263335,"name":"Moderately-differentiated thymic neuroendocrine carcinoma","type":"Histopathological subtype"},{"orpha":263339,"name":"Poorly differentiated thymic neuroendocrine carcinoma","type":"Histopathological subtype"},{"orpha":263331,"name":"Well-differentiated thymic neuroendocrine carcinoma","type":"Histopathological subtype"}],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":null}