raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:263331

Well-differentiated thymic neuroendocrine carcinoma

Type
Histopathological subtype
Group
Subtype of disorder
Inheritance
Not applicable
Age of onset
Adult
Status
active

This disease is described under Thymic neuroendocrine carcinoma

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enWell-differentiated thymic neuroendocrine carcinoma
frCarcinome neuroendocrine thymique bien différenciéCNET bien différencié
deThymuskarzinom, neuroendokrines, gut-differenziert
esCarcinoma neuroendocrino tímico bien diferenciado
itCarcinoma neuroendocrino timico ben differenziato
nlGoed gedifferentieerd neuro-endocrien thymuscarcinoom
ptCarcinoma neuroendócrino tímico bem-diferenciado
plDobrze zróżnicowany rak neuroendokrynny grasicy
csDobře diferencovaný neuroendokrinní karcinom thymu
ukДобре диференційована нейроендокринна карцинома тимуса
zh高分化胸腺神经内分泌癌
trİyi diferansiye timik nöroendokrin karsinom
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10C37NTBTattributedvalidated
ICD-112C27.1NTBTindexvalidated
MONDO0016976Evalidated
UMLSC4305465Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

1 record
TypeClassValueAreaQualificationValidationSource
Point prevalenceUnknown—WorldwideClass onlyNot yet validatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card