ORPHA:92
Juvenile idiopathic arthritis
Synonyms: Juvenile chronic arthritis · Juvenile rheumatoid arthritis
- Type
- Clinical group
- Group
- Group of disorders
- Age of onset
- Childhood
- Status
- active
A rare, heterogeneous group of rheumatologic diseases characterized by arthritis which has an onset before 16 years of age, persists for more than 6 weeks, and is of unknown origin.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Juvenile idiopathic arthritis | Juvenile chronic arthritis · Juvenile rheumatoid arthritis |
| fr | Arthrite juvénile idiopathique | Arthrite juvénile chronique · Arthrite juvénile rhumatoïde |
| de | Arthritis, idiopathische juvenile | Arthritis, chronische juvenile · Arthritis, juvenile rheumatische |
| es | Artritis idiopática juvenil | Artritis crónica juvenil · Artritis reumatoide juvenil |
| it | Artrite idiopatica giovanile | Artrite cronica giovanile · Artrite reumatoide giovanile |
| nl | Juveniele idiopathische artritis | Juveniele chronische artritis · Juveniele reumatoïde artritis |
| pt | Artrite juvenil idiopática | Artrite crónica juvenil · Artrite reumatóide juvenil · Doença de Still |
| pl | Młodzieńcze idiopatyczne zapalenie stawów | Młodzieńcze przewlekłe zapalenie stawów · Młodzieńcze reumatoidalne zapalenie stawów |
| cs | Juvenilní idiopatická artritida | Juvenilní chronická artritida · Juvenilní revmatoidní artritida |
| uk | Ювенільний ідіопатичний артрит | Ювенільний хронічний артрит · Ювенільний ревматоїдний артрит |
| zh | 青少年特发性关节炎 | 幼年型类风湿性关节炎 |
| tr | Jüvenil idiopatik artriti | jüvenil kronik artrit · jüvenil romatoid artrit |
Definition in:
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-11 | FA24 | E | specific | validated |
| MONDO | 0011429 | E | validated | |
| MONDO | 11429 | E | validated | |
| MeSH | D001171 | E | validated | |
| UMLS | C3495559 | E | validated | |
| MedDRA | 10059176 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (3):
- ORPHA:486955Rare pediatric rheumatologic disease
rare systemic or rheumatologic diseases of childhood - ORPHA:182231Rare rheumatologic disease
rare systemic and rheumatological diseases - ORPHA:264704Secondary interstitial lung disease specific to childhood associated with a connective tissue disease
rare respiratory diseases; rare transplant-related disorders
Children (6):
- ORPHA:85438Enthesitis-related juvenile idiopathic arthritis
- ORPHA:85410Oligoarticular juvenile idiopathic arthritis
- ORPHA:404580Polyarticular juvenile idiopathic arthritis
- ORPHA:85436Psoriasis-related juvenile idiopathic arthritis
- ORPHA:85414Systemic-onset juvenile idiopathic arthritis
- ORPHA:91140Unspecified juvenile idiopathic arthritis
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
8 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | 1-5 / 10 000 | 13 / 100 000 | Czech Republic | Value and class | Validated | 17181917[PMID] |
| Annual incidence | 1-9 / 100 000 | 1.5 / 100 000 | Europe | Value and class | Validated | [EXPERT]_ORPHANET |
| Point prevalence | 1-9 / 100 000 | 4.7 / 100 000 | France | Value and class | Validated | Haute Autorité de Santé 2009[OTHER]_ORPHANET_16821272[PMID] |
| Point prevalence | 1-9 / 100 000 | 8.9 / 100 000 | United States | Value and class | Not yet validated | 23588938[PMID]_ORPHANET |
| Point prevalence | 1-5 / 10 000 | 21 / 100 000 | Czech Republic | Value and class | Not yet validated | 17181917[PMID]_ORPHANET |
| Point prevalence | 1-5 / 10 000 | 20.5 / 100 000 | Worldwide | Value and class | Validated | 24210707[PMID] |
| Point prevalence | 6-9 / 10 000 | 74.6 / 100 000 | Specific population | Value and class | Validated | 31150159[PMID] |
| Annual incidence | 1-9 / 100 000 | 7.8 / 100 000 | Worldwide | Value and class | Validated | 24210707[PMID] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/92
- This record as JSON: /data/d/92.json