Polyarticular juvenile idiopathic arthritis
Synonyms: Juvenile polyarthritis · Juvenile polyarticular arthritis · Polyarticular JIA
- Type
- Clinical group
- Group
- Group of disorders
- Status
- active
A rare type of juvenile idiopathic arthritis characterized by arthritis with an onset prior to the age of 16 years persisting for longer than six weeks and affecting at least five joints during the first six months of the disease. Other possible causes of joint inflammation must be excluded. Two subgroups of the disease can be distinguished, based on the presence of absence of rheumatoid factor. Both subgroups are more common in girls and may be associated with mild fever, weight loss, anemia, moderate hepatosplenomegaly, and mild growth retardation.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Polyarticular juvenile idiopathic arthritis | Juvenile polyarthritis · Juvenile polyarticular arthritis · Polyarticular JIA |
| fr | Arthrite juvénile idiopathique polyarticulaire | AJI polyarticulaire · Polyarthrite juvénile |
| de | Arthritis, idiopathische juvenile, polyartikuläre | Juvenile Polyarthritis · Polyartikuläre JIA · Polyartikuläre juvenile Arthritis |
| es | Artritis idiopática juvenil poliarticular | AIJ poliarticular · Artritis juvenil poliarticular · Poliartritis juvenil |
| it | Poliartrite giovanile idiopatica | Artrite poliarticolare giovanile |
| nl | Polyarticulaire juveniele idiopathische artritis | Juveniele polyarticulaire artritis · Juveniele polyartritis · Polyarticulaire JIA |
| pt | Poliartrite juvenil | |
| pl | Młodzieńcze idiopatyczne zapalenie wielostawowe | Wielostawowe JIA · Młodzieńcze zapalenie wielostawowe · Młodzieńcze zapalenie wielostawowe |
| cs | Juvenilní polyartritida | Juvenilní polyartikulární artritida |
| uk | Полісуглобовий ювенільний ідіопатичний артрит | Ювенільний поліартрит · Ювенільний поліартикулярний артрит · Поліартикулярний ЮІА |
| zh | 多关节青少年特发性关节炎 | 幼年多发性关节炎 |
| tr | Poliartiküler juvenil idiyopatik artrit | Poliartiküler JIA · jüvenil poliartrit · jüvenil poliartiküler artrit |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| MONDO | 0018456 | E | validated | |
| MONDO | 18456 | E | validated | |
| UMLS | C4521004 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:92Juvenile idiopathic arthritis
rare respiratory diseases; rare systemic and rheumatological diseases; rare systemic or rheumatologic diseases of childhood; rare transplant-related disorders
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/404580
- This record as JSON: /data/d/404580.json