raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:91140

Unspecified juvenile idiopathic arthritis

Synonyms: Unspecified JIA

Type
Disease
Group
Disorder
Age of onset
Childhood, Infancy
Status
active

Unspecified juvenile idiopathic arthritis is a rare, pediatric, rheumatologic disease, a subtype of juvenile idiopathic arthritis (JIA) characterized by arthritis of an unknown cause that persists for at least 6 weeks, and does not fulfill the criteria for any of the other JIA subtypes, or fulfills criteria for more than one of the other subtypes.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enUnspecified juvenile idiopathic arthritisUnspecified JIA
frArthrite juvénile idiopathique indéterminéeAJI indéterminée
deArthritis, idiopathische juvenile, unklassifizierteUndifferenzierte JIA
esArtritis idiopática juvenil no específicaAIJ no específica
itArtrite idiopatica giovanile aspecifica
nlNiet-gespecificeerde juveniele idiopathische artritisNiet-gespecificeerde JIA
ptArtrite idiopática juvenil, não-classificada
plNiespecyficzne młodzieńcze idiopatyczne zapalenie stawówNiespecyficzne JIA
csNeklasifikovaná juvenilní idiopatická artritida= en
ukНеуточнений ювенільний ідіопатичний артритНевизначений JIA
zh不明青少年特发性关节炎不明青少年特发性关节炎
trTanımlanmamış juvenil idiyopatik artritTanımlanmamış JIA

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10M08.8NTBTattributedvalidated
ICD-11FA24.YNTBTattributedvalidated
MONDO0019607Evalidated
UMLSC5680196Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

  • ORPHA:92Juvenile idiopathic arthritis
    rare respiratory diseases; rare systemic and rheumatological diseases; rare systemic or rheumatologic diseases of childhood; rare transplant-related disorders

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

1 record
TypeClassValueAreaQualificationValidationSource
Point prevalenceUnknown—WorldwideClass onlyValidatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card