Vulvar carcinoma
Synonyms: Carcinoma of vulva
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adult, Elderly
- Status
- active
A group of rare tumors of the vulva comprising HPV-associated and HPV-independent squamous cell carcinomas as the most frequent malignant vulvar tumors, basal cell carcinomas, adenocarcinomas, and Bartholin gland carcinomas. Depending on the type of tumor and disease stage, patients may present with a painless vulvar mass or ulcer, or with pruritus, a burning sensation, pain, or bleeding.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Vulvar carcinoma | Carcinoma of vulva |
| fr | Carcinome de la vulve | Carcinome vulvaire |
| de | Vulvakarzinom | Karzinom der Vulva |
| es | Carcinoma vulvar | Carcinoma de la vulva |
| it | Carcinoma vulvare | |
| nl | Vulvacarcinoom | Carcinoom van vulva |
| pt | Carcinoma vulvar | |
| pl | Rak sromu | Rak warg sromowych i łechtaczki |
| cs | Karcinom vulvy | = en |
| uk | Карцинома вульви | Карцинома вульви |
| zh | 外阴癌 | = en |
| tr | Vulvar karsinom | Vulva karsinomu |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C51.8 | E | specific | not yet validated |
| ICD-11 | 2C70 | E | specific | validated |
| MONDO | 0005215 | E | validated | |
| UMLS | C0677055 | E | validated | |
| GARD | 9349 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:180312Rare vulvovaginal tumor
rare neoplastic diseases; rare gynecological and obstetric diseases
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | 1-9 / 1 000 000 | 0.86 / 100 000 | Worldwide | Value and class | Validated | 37531169[PMID]_ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/494418
- This record as JSON: /data/d/494418.json