Vulvar squamous cell carcinoma
Synonyms: Squamous cell carcinoma of the vulva
- Type
- Histopathological subtype
- Group
- Subtype of disorder
- Inheritance
- Not applicable
- Age of onset
- Adult, Elderly
- Status
- active
A rare vulvar carcinoma characterized by an ulcer, nodule, macule, or pedunculated mass which is histologically composed of infiltrating islands of malignant squamous cells. Histological subtypes include keratinizing, non-keratinizing, basaloid, warty, and verrucous carcinomas. Some tumors are associated with human papilloma virus, smoking, high grade squamous intraepithelial lesion, chronic vulvar inflammatory disorders, or differentiated vulvar intraepithelial neoplasia. Patients may present with discharge, bleeding, or pain. Most important prognostic features are tumor depth and lymph node status.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Vulvar squamous cell carcinoma | Squamous cell carcinoma of the vulva |
| fr | Carcinome épidermoïde de la vulve | Carcinome épidermoïde vulvaire |
| de | Plattenepithelkarzinom der Vulva | Squamöses Zellkarzinom der Vulva · Vulvakarzinom, squamöses |
| es | Carcinoma de células escamosas de vulva | |
| it | Carcinoma vulvare a cellule squamose | |
| nl | Plaveiselcelcarcinoom van vulva | Vulvair plaveiselcelcarcinoom |
| pt | Carcinoma de células escamosas vulvares | Carcinoma espinocelular vulvar |
| pl | Rak płaskonabłonkowy sromu | Rak płaskonabłonkowy warg sromowych i łechtaczki |
| cs | Dlaždicobuněčný (spinocelulární) karcinom vulvy | = en |
| uk | Плоскоклітинний рак вульви | Плоскоклітинний рак вульви |
| zh | 外阴鳞状细胞癌 | = en |
| tr | Vulvar skuamöz hücreli karsinom | Vulvanın skuamöz hücreli karsinomu |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C51.8 | NTBT | attributed | validated |
| ICD-11 | 2C70.2 | E | specific | validated |
| MONDO | 0024609 | E | validated | |
| UMLS | C0280856 | E | validated | |
| MedDRA | 10041875 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:494418Vulvar carcinoma
rare neoplastic diseases; rare gynecological and obstetric diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/494448
- This record as JSON: /data/d/494448.json