Vulvar adenocarcinoma
Synonyms: Adenocarcinoma of the vulva
- Type
- Histopathological subtype
- Group
- Subtype of disorder
- Inheritance
- Not applicable
- Age of onset
- Adult, Elderly
- Status
- active
A rare vulvar carcinoma characterized by a malignant epithelial neoplasm of glandular origin and/or with glandular characteristics arising in the vulva, including adenocarcinoma of mammary gland type, sweat gland type, and intestinal type, as well as adenocarcinomas of the Bartholin glands and Paget disease of the vulva. Depending on the type of tumor and disease stage, patients may present with a solitary vulvar mass, bleeding, or (in the case of Paget disease) a pruritic, erythematous, eczematous lesion.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Vulvar adenocarcinoma | Adenocarcinoma of the vulva |
| fr | Adénocarcinome de la vulve | Adénocarcinome vulvaire |
| de | Adenokarzinom der Vulva | |
| es | Adenocarcinoma vulvar | Adenocarcinoma de la vulva |
| it | Adenocarcinoma vulvare | |
| nl | Adenocarcinoom van vulva | |
| pt | Adenocarcinoma vulvar | |
| pl | Rak gruczołowy sromu | Gruczolak złośliwy sromu |
| cs | Adenokarcinom vulvy | = en |
| uk | Аденокарцинома вульви | Аденокарцинома вульви |
| zh | 外阴腺癌 | = en |
| tr | Vulvar adenokarsinom | Vulvanın adenokarsinomu |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C51.8 | NTBT | attributed | validated |
| MONDO | 0024336 | E | validated | |
| UMLS | C1336975 | E | validated | |
| MedDRA | 10063536 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:494418Vulvar carcinoma
rare neoplastic diseases; rare gynecological and obstetric diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/494454
- This record as JSON: /data/d/494454.json