Vulvar basal cell carcinoma
Synonyms: Basal cell carcinoma of vulva
- Type
- Histopathological subtype
- Group
- Subtype of disorder
- Inheritance
- Not applicable
- Age of onset
- Adult, Elderly
- Status
- active
A rare vulvar carcinoma characterized by a slowly growing ulcer or nodule which is histologically composed of demarcated nests of palisaded basal cells originating at the epidermal-dermal junction. Occasionally, the tumor may be extensively pigmented. Patients most commonly present with pruritus. The lesion is usually treated by local excision, although groin metastases have been reported.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Vulvar basal cell carcinoma | Basal cell carcinoma of vulva |
| fr | Carcinome basocellulaire de la vulve | Carcinome basocellulaire vulvaire |
| de | Basalzellkarzinom der Vulva | |
| es | Carcinoma de células basales de la vulva | |
| it | Carcinoma della vulva a cellule basali | |
| nl | Basaalcelcarcinoom van vulva | |
| pt | Carcinoma basocelular vulvar | |
| pl | Rak podstawnokomórkowy sromu | Rak podstawnokomórkowy warg sromowych i łechtaczki |
| cs | Bazocelulární karcinom vulvy | = en |
| uk | Базальноклітинна карцинома вульви | Базальноклітинна карцинома вульви |
| zh | 外阴基底细胞癌 | = en |
| tr | Vulvar bazal hücreli karsinom | Vulvanın bazal hücreli karsinomu |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C51.8 | NTBT | attributed | validated |
| ICD-11 | 2C70.0 | E | specific | validated |
| MONDO | 0002955 | E | validated | |
| UMLS | C1336977 | E | validated | |
| MedDRA | 10082639 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:494418Vulvar carcinoma
rare neoplastic diseases; rare gynecological and obstetric diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/494451
- This record as JSON: /data/d/494451.json