ORPHA:36388
Paraneoplastic neurologic syndrome
Synonyms: PNS
- Type
- Category
- Group
- Group of disorders
- Inheritance
- Not applicable
- Age of onset
- All ages
- Status
- active
Paraneoplastic neurological syndromes (PNS) can be defined as remote effects of cancer that are not caused by the tumor and its metastasis, or by infection, ischemia or metabolic disruptions.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Paraneoplastic neurologic syndrome | PNS |
| fr | Syndrome neurologique paranéoplasique | = en |
| de | Paraneoplastische Neurologische Syndrome | PCD · PNS · Paraneoplastische zerebelläre Degeneration |
| es | Síndrome neurológico paraneoplásico | |
| it | Sindrome neurologica paraneoplastica | = en |
| nl | Paraneoplastisch neurologisch syndroom | = en |
| pt | Síndrome neurológico paraneoplásico | = en |
| pl | Neurologiczny zespół paraneoplastyczny | Paraneoplastyczne zwyrodnienie mózgu · PCD · PNS · Neurologiczny zespół paranowotworowy |
| cs | Paraneoplastické neurologické syndromy | PCD · PNS · Paraneoplastická cerebelární degenerace |
| uk | Паранеопластичний неврологічний синдром | = en |
| zh | 神经系统副肿瘤综合征 | 副肿瘤性小脑变性 |
| tr | Paraneoplastik nörolojik sendrom | PCD · PNS · Paraneoplastik serebellar dejenerasyon |
Definition in:
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| MONDO | 0018215 | E | validated | |
| MONDO | 18215 | E | validated | |
| MeSH | D020361 | E | validated | |
| UMLS | C0751911 | E | validated | |
| MedDRA | 10072106 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:98006Rare neurologic disease
rare neurological diseases
Children (10):
- ORPHA:623615Autoimmune limbic encephalitis
- ORPHA:71505Cancer-associated retinopathy
- ORPHA:43393Lambert-Eaton myasthenic syndrome
- ORPHA:624166Non-specific autoimmune supratentorial encephalitis with characteristic antibodies
- ORPHA:624178Non-specific autoimmune supratentorial encephalitis without characteristic antibodies
- ORPHA:1183Opsoclonus-myoclonus syndrome
- ORPHA:715850Paraneoplastic acute exudative polymorphous vitelliform maculopathy
- ORPHA:623626Paraneoplastic cerebellar degeneration
- ORPHA:624190Paraneoplastic isolated brainstem encephalitis
- ORPHA:208999Paraneoplastic sensory ganglionopathy
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/36388
- This record as JSON: /data/d/36388.json