{"orpha":36388,"name":"Paraneoplastic neurologic syndrome","type":"Category","group":"Group of disorders","status":"active","flags":[],"synonyms":["PNS"],"definition":"Paraneoplastic neurological syndromes (PNS) can be defined as remote effects of cancer that are not caused by the tumor and its metastasis, or by infection, ischemia or metabolic disruptions.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-36388/","orphanet_url":"https://www.orpha.net/en/disease/detail/36388","names":{"fr":{"name":"Syndrome neurologique paranéoplasique","synonyms":["PNS"],"definition":"Les syndromes neurologiques paranéoplasiques (SNP) peuvent être définis comme des effets à distance d'un cancer qui ne sont causés ni par la tumeur ou ses métastases, ni par une infection, une ischémie ou des perturbations métaboliques."},"de":{"name":"Paraneoplastische Neurologische Syndrome","synonyms":["PCD","PNS","Paraneoplastische zerebelläre Degeneration"],"definition":"Die Paraneoplastischen neurologischen Syndrome (PNS) können definiert werden als Fernwirkung von Malignomen, die nicht durch den Tumor selbst, seine Metastasen, durch Infektion, Ischaemie oder Stoffwechsel-Entgleisungen verursacht sind."},"es":{"name":"Síndrome neurológico paraneoplásico","definition":"El síndrome neurológico paraneoplástico (PNS) puede definirse como los efectos colaterales de un cáncer que no están provocados de forma directa por el mismo, por sus metástasis o por infecciones, por isquemia o por alteraciones metabólicas."},"it":{"name":"Sindrome neurologica paraneoplastica","synonyms":["PNS"]},"nl":{"name":"Paraneoplastisch neurologisch syndroom","synonyms":["PNS"],"definition":"Paraneoplastische neurologische syndromen (PNS) kunnen gedefinieerd worden als effecten op afstand van kanker die niet veroorzaakt worden door de tumor en uitzaaiingen ervan, of door infectie, ischemie of metabole stoornissen."},"pt":{"name":"Síndrome neurológico paraneoplásico","synonyms":["PNS"]},"pl":{"name":"Neurologiczny zespół paraneoplastyczny","synonyms":["Paraneoplastyczne zwyrodnienie mózgu","PCD","PNS","Neurologiczny zespół paranowotworowy"]},"cs":{"name":"Paraneoplastické neurologické syndromy","synonyms":["PCD","PNS","Paraneoplastická cerebelární degenerace"]},"uk":{"name":"Паранеопластичний неврологічний синдром","synonyms":["PNS"],"definition":"Paraneoplastic neurological syndromes (PNS) can be defined as remote effects of cancer that are not caused by the tumor and its metastasis, or by infection, ischemia or metabolic disruptions."},"zh":{"name":"神经系统副肿瘤综合征","synonyms":["副肿瘤性小脑变性"]},"tr":{"name":"Paraneoplastik nörolojik sendrom","synonyms":["PCD","PNS","Paraneoplastik serebellar dejenerasyon"]}},"xrefs":[{"source":"MONDO","code":"0018215","qualifier":"E","icd_relation":null,"validated":true},{"source":"MONDO","code":"18215","qualifier":"E","icd_relation":null,"validated":true},{"source":"MeSH","code":"D020361","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0751911","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10072106","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98006,"name":"Rare neurologic disease"},"parents":[{"orpha":98006,"name":"Rare neurologic disease","classifications":[181]}],"children":[{"orpha":623615,"name":"Autoimmune limbic encephalitis","type":"Disease"},{"orpha":71505,"name":"Cancer-associated retinopathy","type":"Disease"},{"orpha":43393,"name":"Lambert-Eaton myasthenic syndrome","type":"Disease"},{"orpha":624166,"name":"Non-specific autoimmune supratentorial encephalitis with characteristic antibodies","type":"Disease"},{"orpha":624178,"name":"Non-specific autoimmune supratentorial encephalitis without characteristic antibodies","type":"Disease"},{"orpha":1183,"name":"Opsoclonus-myoclonus syndrome","type":"Disease"},{"orpha":715850,"name":"Paraneoplastic acute exudative polymorphous vitelliform maculopathy","type":"Clinical subtype"},{"orpha":623626,"name":"Paraneoplastic cerebellar degeneration","type":"Disease"},{"orpha":624190,"name":"Paraneoplastic isolated brainstem encephalitis","type":"Disease"},{"orpha":208999,"name":"Paraneoplastic sensory ganglionopathy","type":"Disease"}],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["All ages"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}