raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:208999

Paraneoplastic sensory ganglionopathy

Synonyms: Paraneoplastic sensory neuronopathy

Type
Disease
Group
Disorder
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enParaneoplastic sensory ganglionopathyParaneoplastic sensory neuronopathy
frGanglionopathie sensitive paranéoplasiqueNeuronopathie sensitive paranéoplasique
deGanglionopathie, paraneoplastische sensorischeNeuropathie, paraneoplastische sensorische
esGanglionopatía sensitiva paraneoplásicaNeuropatía sensitiva paraneoplásica
itGanglionopatia sensitiva paraneoplasticaNeuropatia sensitiva paraneoplastica
nlParaneoplastische sensorische ganglionopathieParaneoplastische sensorische neuronopathie
ptGanglionopatia sensitiva paraneoplásica
plParaneoplastyczna gangliopatia czuciowaParaneoplastyczna neuropatia czuciowa
csParaneoplastická senzorická ganglionopatieParaneoplastická senzitivní neuronopatie
ukПаранеопластична сенсорна гангліонопатіяПаранеопластична сенсорна нейронопатія
zh副肿瘤性感觉神经节病副肿瘤性感觉神经元病
trParaneoplastik duyusal ganglionopatiParaneoplastik duyusal nöronopati
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10G60.8NTBTattributedvalidated
ICD-118E4A.1NTBTindexvalidated
MONDO0016174Evalidated
UMLSC5679792Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (2):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

22 annotations · validated 2025-06-27
HPOTerm (as annotated by Orphanet)Diagnostic
Frequent (79-30%)
HP:5000016Anti-Hu antibody positivity
HP:0002075Dysdiadochokinesis
HP:0012534Dysesthesia
HP:0001310Dysmetria
HP:0032147Erythromelalgia
HP:0002066Gait ataxia
HP:0046505Hand pain
HP:0033660Hand paresthesia
HP:0033748Hypoesthesia
HP:0006886Impaired distal vibration sensation
HP:0010829Impaired temperature sensition
HP:0002311Incoordination
HP:0002403Positive Romberg sign
HP:0001315Reduced tendon reflexes
HP:0010871Sensory ataxia
Occasional (29-5%)
HP:0033125Follicular lymphoma
HP:0012189Hodgkin lymphoma
HP:0030360Large cell lung carcinoma
HP:0100634Neuroendocrine neoplasm
HP:0030357Small cell lung carcinoma
Excluded (0%)
HP:0430058Anti-herpes simplex antibody positivity
HP:0100502Decreased circulating vitamin B12 concentration

Annotation source: 24385818[PMID]_35272731[PMID]

7

Sources for this card