ORPHA:35807
Malignant germ cell tumor of ovary
Synonyms: MOGCT · Malignant ovarian germ cell tumor · Ovarian germ cell cancer
- Type
- Category
- Group
- Group of disorders
- Inheritance
- Unknown
- Age of onset
- Adolescent, Adult, Childhood, Elderly, Infancy
- Status
- active
Malignant germ cell tumor of ovary is a rare ovarian cancer arising from germ cells in the ovary, frequently unilateral at diagnosis which characteristically presents during adolescence with pelvic mass, fever, vaginal bleeding and acute abdomen.
1
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Malignant germ cell tumor of ovary | MOGCT · Malignant ovarian germ cell tumor · Ovarian germ cell cancer |
| fr | Tumeur maligne ovarienne germinale | Cancer germinal de l'ovaire · MOGCT |
| de | Maligne Keimzelltumoren des Ovars | Keimzelltumor, maligner ovarieller · MOGCT |
| es | Tumor maligno de ovario de células germinales | Cáncer de ovario de células germinales · MOGCT · Tumor maligno ovárico de células germinales |
| it | Tumore maligno dell'ovaio a cellule germinali | Cancro ovarico a cellule germinali · MOGCT · Tumore ovarico maligno a cellule germinali |
| nl | Maligne kiemceltumor van ovarium | MOGCT · Maligne kiemceltumor van eierstok · Maligne ovariële kiemceltumor · Ovariële kiemceltumor |
| pt | Tumor maligno das células da linha germinativa do ovário | |
| pl | Złośliwy nowotwór komórek germinalnych jajnika | MOGCT · Rak komórek germinalnych jajnika |
| cs | Maligní germinální nádory ovaria | MOGCT · Maligní ovariální germinální nádor · Ovariální germinální rakovina |
| uk | Злоякісна герміногенна пухлина яєчника | Злоякісна герміногенна пухлина яєчників · MOGCT · Рак зародкових клітин яєчників |
| zh | 恶性卵巢生殖细胞肿瘤 | 卵巢恶性生殖细胞肿瘤 |
| tr | Yumurtalıkların habis germ hücreli tümörü | MOGCT · Yumurtalık germ hücre kanseri · Habis yumurtalık germ hücre tümörü |
Definition in:
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| OMIM | 603737 | E | validated | |
| ICD-11 | 2C73.Y | NTBT | index | validated |
| MONDO | 0018171 | E | validated | |
| MONDO | 18171 | E | validated | |
| MeSH | C562841 | E | validated | |
| UMLS | C0346180 | E | validated | |
| GARD | 9330 | E | validated | |
| MedDRA | 10061893 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
3
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (2):
- ORPHA:363582Gonadal germ cell tumor
rare neoplastic diseases; rare transplant-related disorders - ORPHA:398940Malignant non-epithelial tumor of ovary
rare neoplastic diseases; rare gynecological and obstetric diseases
4
Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
27 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | <1 / 1 000 000 | 0.08 / 100 000 | Europe | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Lifetime Prevalence | 1-9 / 100 000 | 2.3 / 100 000 | Europe | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | 1-9 / 1 000 000 | 0.2 / 100 000 | United States | Value and class | Validated | 15863154[PMID] |
| Point prevalence | Unknown | — | Worldwide | Class only | Validated | ORPHANET |
| Annual incidence | <1 / 1 000 000 | 0.072 / 100 000 | Austria | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.07 / 100 000 | Belgium | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.089 / 100 000 | Bulgaria | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.093 / 100 000 | Croatia | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.087 / 100 000 | Czech Republic | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.062 / 100 000 | Finland | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.065 / 100 000 | Germany | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.085 / 100 000 | Iceland | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.065 / 100 000 | Ireland | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.065 / 100 000 | Italy | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.081 / 100 000 | Latvia | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.095 / 100 000 | Lithuania | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.09 / 100 000 | Norway | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.098 / 100 000 | Poland | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.064 / 100 000 | Portugal | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.075 / 100 000 | Slovenia | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.072 / 100 000 | Spain | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.051 / 100 000 | Switzerland | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.061 / 100 000 | Netherlands | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | <1 / 1 000 000 | 0.064 / 100 000 | United Kingdom | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | 1-9 / 1 000 000 | 0.157 / 100 000 | Estonia | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | 1-9 / 1 000 000 | 0.126 / 100 000 | Malta | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
| Annual incidence | 1-9 / 1 000 000 | 0.141 / 100 000 | Slovakia | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
7
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/35807
- This record as JSON: /data/d/35807.json