Primary non-gestational choriocarcinoma of ovary
Synonyms: NGCO · Primary non-gestational ovarian choriocarcinoma
- Type
- Disease
- Group
- Disorder
- Inheritance
- Unknown
- Age of onset
- Adolescent
- Status
- active
Primary non-gestational choriocarcinoma of ovary is a rare ovarian germ cell malignant tumor, arising from primordial germ cells, usually presenting with nausea, vomiting, abdominal pain, menstrual irregularities, and characterized by fast growth pattern, metastasis to lung, liver and brain and production of human chorionic gonadotrophin (hCG). It is apparently chemoresistant and has a worse prognosis than gestational choriocarcinoma and hence should be distinguished from the latter by DNA polymorphism.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Primary non-gestational choriocarcinoma of ovary | NGCO · Primary non-gestational ovarian choriocarcinoma |
| fr | Choriocarcinome ovarien primitif non gestationnel | Choriocarcinome primitif non gestationnel de l'ovaire · NGCO |
| de | Primäres nicht-gestationales Chorionkarzinom des Ovars | NGCO · Ovarielles Chorionkarzinom, nicht-gestationales primäres · Primäres Chorionkarzinom des Ovars · Primäres nicht-gestationales ovarielles Chorionkarzinom |
| es | Coriocarcinoma primario no gestacional de ovario | Coriocarcinoma ovárico primario no gestacional · NGCO |
| it | Coriocarcinoma dell'ovaio non gestazionale primitivo | Coriocarcinoma ovarico non gestazionale primitivo · NGCO |
| nl | Primair niet-gestationeel choriocarcinoom van ovarium | NGCO · Primair niet-gestationeel choriocarcinoom van eierstok · Primair niet-gestationeel ovarieel choriocarcinoom |
| pt | Coriocarcinoma ovárico não gestacional | NGCO |
| pl | Pierwotny nieciążowy rak kosmówkowy jajnika | NGCO |
| cs | Primární non-gestační choriokarcinom ovária | NGCO · Primární non-gestační ovariální choriokarcinom |
| uk | Первинна негестаційна хоріокарцинома яєчника | NGCO · Первинна негестаційна хоріокарцинома яєчників |
| zh | 原发性非妊娠卵巢绒毛膜癌 | 卵巢原发性非妊娠性绒毛膜癌 |
| tr | Yumurtalıkların primer gestasyonel olmayan koryokarsinomu | NGCO · Primer gebelik dışı yumurtalık koriyokarsinomu |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C56 | NTBT | attributed | validated |
| ICD-11 | 2C73.Y | NTBT | index | validated |
| MONDO | 0017327 | E | validated | |
| UMLS | C4274424 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:35807Malignant germ cell tumor of ovary
rare neoplastic diseases; rare gynecological and obstetric diseases; rare transplant-related disorders
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/289356
- This record as JSON: /data/d/289356.json