Malignant non-dysgerminomatous germ cell tumor of ovary
Synonyms: Non-dysgerminomatous germ cell cancer of ovary
- Type
- Disease
- Group
- Disorder
- Inheritance
- Unknown
- Age of onset
- Adolescent
- Status
- active
Malignant non-dysgerminomatous germ cell tumor of ovary is a rare malignant germ cell tumor of ovary arising from germ cells in the ovary, frequently unilateral at diagnosis, usually presenting during adolescence with pelvic mass, fever, vaginal bleeding and acute abdomen, with certain subtypes being occasionally associated with isosexual precocity, virilization, hyperthyroidism or carcinoid syndrome. Histologically they comprise the following: embryonal carcinoma, Yolk sac tumor, polyembryoma and mixed germ cell tumor.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Malignant non-dysgerminomatous germ cell tumor of ovary | Non-dysgerminomatous germ cell cancer of ovary |
| fr | Tumeur germinale maligne non dysgerminomateuse de l'ovaire | Cancer germinal non dysgerminomateux de l'ovaire |
| de | Keimzelltumor des Ovars, nicht-dysgerminomatöser maligner | Nicht-dysgerminomatöser Keimzellkrebs des Ovars |
| es | Tumor maligno de células germinales no disgerminomatoso de ovario | Cáncer de células germinales no disgerminomatoso de ovario |
| it | Tumore non disgerminale maligno dell'ovaio a cellule germinali | Cancro non disgerminomatoso a cellule germinali · Tumore non disgerminale dell'ovaio a cellule germinali |
| nl | Maligne niet-dysgerminomateuze kiemceltumor van ovarium | Kwaadaardige niet-dysgerminomateuze kiemceltumor van eierstok · Niet-dysgerminomateuze kiemcelkanker van ovarium |
| pt | Tumor de células germinativas ováricas, não-disgerminoma | |
| pl | Malignant non-dysgerminomatous germ cell tumor of ovary | = en |
| cs | Maligní non-dysgerminomový tumor z germinálních buněk ovarií | Non-dysgerminomatózní nádor z germinálních buněk ovarií |
| uk | Злоякісна недисгерміноматозна герміногенна пухлина яєчника | Недисгерміноматозний герміногенний рак яєчника |
| zh | 卵巢恶性非生殖细胞瘤 | 卵巢非无性细胞瘤性生殖细胞癌 |
| tr | Habis over non-disgerminomatöz germ hücre tümörü | Yumurtalık disgerminomatöz olmayan germ hücreli kanser |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C56 | NTBT | attributed | validated |
| ICD-11 | 2C73.Y | NTBT | index | validated |
| MONDO | 0016096 | E | validated | |
| UMLS | C5679783 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:35807Malignant germ cell tumor of ovary
rare neoplastic diseases; rare gynecological and obstetric diseases; rare transplant-related disorders
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/206538
- This record as JSON: /data/d/206538.json