ORPHA:166775
Rare hemorrhagic disorder due to an acquired coagulation factor defect
Synonyms: Rare bleeding disorder due to an acquired coagulation factor defect · Rare coagulopathy due to an acquired coagulation factor defect
- Type
- Category
- Group
- Group of disorders
- Status
- active
This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.
1
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Rare hemorrhagic disorder due to an acquired coagulation factor defect | Rare bleeding disorder due to an acquired coagulation factor defect · Rare coagulopathy due to an acquired coagulation factor defect |
| fr | Maladie hémorragique rare par déficit acquis en facteurs de coagulation | Coagulopathie rare par déficit acquis en facteurs de coagulation |
| de | Blutgerinnungsstörung, erworbene | |
| es | Trastorno hemorrágico raro por un defecto adquirido de factores de coagulación | Coagulopatía rara por un defecto adquirido de los factores de coagulación · Trastorno raro de sangrado por un defecto adquirido de los factores de coagulación |
| it | Disturbo emorragico raro da difetto acquisito dei fattori della coagulazione | Coagulopatia rara da difetto acquisito dei fattori della coagulazione |
| nl | Zeldzame hemorragische stoornis door een verworven coagulatiefactordefect | Zeldzame bloedingsstoornis door een verworven coagulatiefactordefect · Zeldzame coagulopathie door een verworven coagulatiefactordefect |
| pt | Defeito adquirido da coagulação | |
| pl | Rzadkie zaburzenia krzepnięcia z powodu nabytego defektu czynnika krzepnięcia | Rare bleeding disorder due to an acquired coagulation factor defect · Rzadka koagulopatia z powodu nabytego defektu czynnika krzepnięcia |
| cs | Vzácná hemoragická porucha způsobená získanou poruchou koagulačního faktoru | Vzácná krvácivá porucha způsobená získanou poruchou koagulačního faktoru · Vzácná koagulopatie způsobená získanou poruchou koagulačního faktoru |
| uk | Рідкісне геморагічне захворювання, зумовлене набутим дефектом фактора згортання крові | Рідкісне порушення згортання крові через набутий дефект фактора коагуляції · Рідкісна коагулопатія внаслідок набутого дефекту фактора згортання крові |
| zh | 获得性凝血因子缺陷所致罕见出血性疾病 | 获得性凝血因子缺陷所致罕见出血障碍 |
| tr | Edinsel bir pıhtılaşma faktörü defektine bağlı nadir hemorajik bozukluk | Edinsel bir pıhtılaşma faktörü kusuruna bağlı nadir koagülopati · Edinsel bir pıhtılaşma faktörü kusuruna bağlı nadir kanama bozukluğu |
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| MONDO | 15662 | E | validated | |
| UMLS | C5679584 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
3
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:248315Rare hemorrhagic disorder due to a coagulation factors defect
rare hematological diseases
Children (9):
- ORPHA:599490Acquired factor V deficiency
- ORPHA:599495Acquired factor VII deficiency
- ORPHA:599501Acquired factor X deficiency
- ORPHA:599507Acquired factor XI deficiency
- ORPHA:599513Acquired factor XIII deficiency
- ORPHA:599480Acquired hemophilia A
- ORPHA:599485Acquired hemophilia B
- ORPHA:26348Acquired prothrombin deficiency
- ORPHA:99147Acquired von Willebrand syndrome
Codes that Orphanet moved or referred to this one:
- ORPHA:73274OBSOLETE: Acquired hemophilia referred to · inactive
4
Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
0 recordsNo prevalence record in this release.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
7
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/166775
- This record as JSON: /data/d/166775.json