raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:166775

Rare hemorrhagic disorder due to an acquired coagulation factor defect

Synonyms: Rare bleeding disorder due to an acquired coagulation factor defect · Rare coagulopathy due to an acquired coagulation factor defect

Type
Category
Group
Group of disorders
Status
active

This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enRare hemorrhagic disorder due to an acquired coagulation factor defectRare bleeding disorder due to an acquired coagulation factor defect · Rare coagulopathy due to an acquired coagulation factor defect
frMaladie hémorragique rare par déficit acquis en facteurs de coagulationCoagulopathie rare par déficit acquis en facteurs de coagulation
deBlutgerinnungsstörung, erworbene
esTrastorno hemorrágico raro por un defecto adquirido de factores de coagulaciónCoagulopatía rara por un defecto adquirido de los factores de coagulación · Trastorno raro de sangrado por un defecto adquirido de los factores de coagulación
itDisturbo emorragico raro da difetto acquisito dei fattori della coagulazioneCoagulopatia rara da difetto acquisito dei fattori della coagulazione
nlZeldzame hemorragische stoornis door een verworven coagulatiefactordefectZeldzame bloedingsstoornis door een verworven coagulatiefactordefect · Zeldzame coagulopathie door een verworven coagulatiefactordefect
ptDefeito adquirido da coagulação
plRzadkie zaburzenia krzepnięcia z powodu nabytego defektu czynnika krzepnięciaRare bleeding disorder due to an acquired coagulation factor defect · Rzadka koagulopatia z powodu nabytego defektu czynnika krzepnięcia
csVzácná hemoragická porucha způsobená získanou poruchou koagulačního faktoruVzácná krvácivá porucha způsobená získanou poruchou koagulačního faktoru · Vzácná koagulopatie způsobená získanou poruchou koagulačního faktoru
ukРідкісне геморагічне захворювання, зумовлене набутим дефектом фактора згортання кровіРідкісне порушення згортання крові через набутий дефект фактора коагуляції · Рідкісна коагулопатія внаслідок набутого дефекту фактора згортання крові
zh获得性凝血因子缺陷所致罕见出血性疾病获得性凝血因子缺陷所致罕见出血障碍
trEdinsel bir pıhtılaşma faktörü defektine bağlı nadir hemorajik bozuklukEdinsel bir pıhtılaşma faktörü kusuruna bağlı nadir koagülopati · Edinsel bir pıhtılaşma faktörü kusuruna bağlı nadir kanama bozukluğu
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
MONDO15662Evalidated
UMLSC5679584Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

Children (9):

Codes that Orphanet moved or referred to this one:

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card