{"orpha":166775,"name":"Rare hemorrhagic disorder due to an acquired coagulation factor defect","type":"Category","group":"Group of disorders","status":"active","flags":[],"synonyms":["Rare bleeding disorder due to an acquired coagulation factor defect","Rare coagulopathy due to an acquired coagulation factor defect"],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-166775/","orphanet_url":"https://www.orpha.net/en/disease/detail/166775","names":{"fr":{"name":"Maladie hémorragique rare par déficit acquis en facteurs de coagulation","synonyms":["Coagulopathie rare par déficit acquis en facteurs de coagulation"]},"de":{"name":"Blutgerinnungsstörung, erworbene"},"es":{"name":"Trastorno hemorrágico raro por un defecto adquirido de factores de coagulación","synonyms":["Coagulopatía rara por un defecto adquirido de los factores de coagulación","Trastorno raro de sangrado por un defecto adquirido de los factores de coagulación"]},"it":{"name":"Disturbo emorragico raro da difetto acquisito dei fattori della coagulazione","synonyms":["Coagulopatia rara da difetto acquisito dei fattori della coagulazione"]},"nl":{"name":"Zeldzame hemorragische stoornis door een verworven coagulatiefactordefect","synonyms":["Zeldzame bloedingsstoornis door een verworven coagulatiefactordefect","Zeldzame coagulopathie door een verworven coagulatiefactordefect"]},"pt":{"name":"Defeito adquirido da coagulação"},"pl":{"name":"Rzadkie zaburzenia krzepnięcia z powodu nabytego defektu czynnika krzepnięcia","synonyms":["Rare bleeding disorder due to an acquired coagulation factor defect","Rzadka koagulopatia z powodu nabytego defektu czynnika krzepnięcia"]},"cs":{"name":"Vzácná hemoragická porucha způsobená získanou poruchou koagulačního faktoru","synonyms":["Vzácná krvácivá porucha způsobená získanou poruchou koagulačního faktoru","Vzácná koagulopatie způsobená získanou poruchou koagulačního faktoru"]},"uk":{"name":"Рідкісне геморагічне захворювання, зумовлене набутим дефектом фактора згортання крові","synonyms":["Рідкісне порушення згортання крові через набутий дефект фактора коагуляції","Рідкісна коагулопатія внаслідок набутого дефекту фактора згортання крові"]},"zh":{"name":"获得性凝血因子缺陷所致罕见出血性疾病","synonyms":["获得性凝血因子缺陷所致罕见出血障碍"]},"tr":{"name":"Edinsel bir pıhtılaşma faktörü defektine bağlı nadir hemorajik bozukluk","synonyms":["Edinsel bir pıhtılaşma faktörü kusuruna bağlı nadir koagülopati","Edinsel bir pıhtılaşma faktörü kusuruna bağlı nadir kanama bozukluğu"]}},"xrefs":[{"source":"MONDO","code":"15662","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5679584","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[{"type":"Referred to","orpha":73274,"name":"OBSOLETE: Acquired hemophilia","status":"inactive"}],"preferential_parent":{"orpha":97992,"name":"Rare hematologic disease"},"parents":[{"orpha":248315,"name":"Rare hemorrhagic disorder due to a coagulation factors defect","classifications":[194]}],"children":[{"orpha":599490,"name":"Acquired factor V deficiency","type":"Disease"},{"orpha":599495,"name":"Acquired factor VII deficiency","type":"Disease"},{"orpha":599501,"name":"Acquired factor X deficiency","type":"Disease"},{"orpha":599507,"name":"Acquired factor XI deficiency","type":"Disease"},{"orpha":599513,"name":"Acquired factor XIII deficiency","type":"Disease"},{"orpha":599480,"name":"Acquired hemophilia A","type":"Disease"},{"orpha":599485,"name":"Acquired hemophilia B","type":"Disease"},{"orpha":26348,"name":"Acquired prothrombin deficiency","type":"Disease"},{"orpha":99147,"name":"Acquired von Willebrand syndrome","type":"Disease"}],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}