raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:599485

Acquired hemophilia B

Synonyms: AHB · Acquired F9 deficiency · Acquired factor IX deficiency

Type
Disease
Group
Disorder
Inheritance
Not applicable
Age of onset
Adult, Childhood, Elderly
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

10 of 12 languages
LangNameSynonyms
enAcquired hemophilia BAHB · Acquired F9 deficiency · Acquired factor IX deficiency
frHémophilie acquise BDéficit acquis en F9 · Déficit acquis en facteur IX
deHämophilie B, erworbeneAHB · F9-Mangel, erworbener · Faktor IX-Mangel, erworbener
esHemofilia B adquiridaDeficiencia adquirida de F9 · Deficiencia adquirida de factor IX · HBA
itEmofilia B acquisitaAHB · Deficit acquisito del fattore IX · Deficit acquisito di F9
nlVerworven hemofilie BAHB · Verworven F9-deficiëntie · Verworven deficiëntie van factor IX
ptHemofilia B adquiridaDeficiência adquirida de F9 · Deficiência adquirida de factor IX · HBA
plNabyta hemofilia BAHB
csZískaná hemofilie B= en
ukНабута гемофілія ВНабута недостатність F9 · Набутий дефіцит фактора IX · AHB
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10D68.4NTBTattributedvalidated
ICD-113B22NTBTindexvalidated
MONDO0035736Evalidated
UMLSC0398609Evalidated
MedDRA10082747Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

2 records
TypeClassValueAreaQualificationValidationSource
Point prevalenceUnknown—WorldwideClass onlyValidatedORPHANET
Annual incidenceUnknown—WorldwideClass onlyValidatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card