Streptococcal toxic-shock syndrome
Synonyms: Streptococcal TSS
- Type
- Etiological subtype
- Group
- Subtype of disorder
- Inheritance
- Not applicable
- Age of onset
- All ages
- Status
- active
Streptococcal toxic-shock syndrome (streptococcal TSS) is an acute disease mediated by the production of superantigenic toxins characterized by the sudden onset of fever and other febrile symptoms, pain, multisystem organ involvement and potentially leading to coma, shock and death due to a <i>Streptococcus pyogenes</i> infection.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Streptococcal toxic-shock syndrome | Streptococcal TSS |
| fr | Syndrome du choc toxique streptococcique | SCT streptococcique |
| de | Toxisches Schock-Syndrom, Streptokokken-induziertes | Streptokokken-TSS |
| es | Síndrome de shock tóxico estreptocócico | Síndrome de shock tóxico por estreptococos · TSS por estreptococos |
| it | Sindrome dello shock tossico da streptococco | TSS da streptococco |
| nl | Streptokokkale toxische shock-syndroom | Streptokokkale TSS |
| pt | Síndrome de choque tóxico estreptocócico | |
| pl | Paciorkowcowy zespół wstrząsu toksycznego | Paciorkowcowy TSS |
| cs | Streptokokový syndrom toxického šoku | Streptokokový TSS |
| uk | Стрептококовий синдром токсичного шоку | Стрептококовий TSS |
| zh | 链球菌中毒性休克综合征 | 链球菌性TSS |
| tr | Streptokoksik toksik şok sendromu | = en |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | A48.3 | NTBT | attributed | validated |
| ICD-11 | 1C45.0 | E | specific | validated |
| MONDO | 0020544 | E | validated | |
| UMLS | C0343532 | E | validated | |
| MedDRA | 10044251 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:36234Bacterial toxic-shock syndrome
rare infectious diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
4 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | 1-9 / 1 000 000 | 0.1 / 100 000 | France | Value and class | Validated | 21976764[PMID]_Dr Lina Gérard[EXPERT] |
| Annual incidence | 1-9 / 1 000 000 | 0.2 / 100 000 | United States | Value and class | Validated | 22534148[PMID]_Dr Lina Gérard[EXPERT] |
| Annual incidence | 1-9 / 1 000 000 | 0.33 / 100 000 | Sweden | Value and class | Validated | 17638193[PMID]_Dr Lina Gérard[EXPERT] |
| Annual incidence | 1-9 / 1 000 000 | 0.23 / 100 000 | Denmark | Value and class | Validated | 15815000[PMID] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/99918
- This record as JSON: /data/d/99918.json