Pulmonary artery coming from patent ductus arteriosus
- Type
- Morphological anomaly
- Group
- Disorder
- Status
- active
Pulmonary artery coming from patent ductus arteriosus is a rare, congenital, non-syndromic heart malformation characterized by the presence of a single (or a double) patent ductus arteriosus which associates one or both pulmonary arteries originating from it. Manifestations are variable, frequently presenting with neonatal cyanosis, severe progressive hypoxia, persistent pulmonary hypertension, increased susceptibility to pulmonary infections, and thoracic asymmetry resulting from asymmetric lung volumes.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Pulmonary artery coming from patent ductus arteriosus | |
| fr | Artère pulmonaire naissant du canal artériel | |
| de | Pulmonalarterie, dem offenem Ductus arteriosus entstammend | |
| es | Arteria pulmonar procedente de ductus arterioso persistente | |
| it | Arteria polmonare ad origine del dotto arterioso pervio | |
| nl | Longslagader afkomstig van open ductus arteriosus | |
| pt | Artéria pulmonar proveniente de canal arterial patente | |
| pl | Tętnica płucna odchodząca od przetrwałego przewodu tętniczego | |
| cs | Plicnice vycházející z ductus arteriosus patens | |
| uk | Легенева артерія, яка відходить від відкритої артеріальної протоки | |
| zh | 起自动脉导管未闭的肺动脉 | |
| tr | Patent duktus arteriyozustan gelen pulmoner arter |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | Q25.7 | NTBT | attributed | validated |
| ICD-11 | LA8B.1 | NTBT | index | validated |
| MONDO | 0020390 | E | validated | |
| UMLS | C3163916 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:1138Abnormal origin of the pulmonary artery
rare developmental anomalies during embryogenesis; rare cardiac malformations
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/99049
- This record as JSON: /data/d/99049.json