raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:1138

Abnormal origin of the pulmonary artery

Type
Clinical group
Group
Group of disorders
Status
active

This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enAbnormal origin of the pulmonary artery
frArtère pulmonaire d'origine anormale
dePulmonalarterie, abnormaler Ursprung
esArteria pulmonar naciente de la aorta
itArteria polmonare ad origine anomala
nlAbnormale oorsprong van arteria pulmonalisAbnormale oorsprong van longslagader
ptArtéria pulmonar com origem na aorta
plNieprawidłowe pochodzenie tętnicy płucnej
csAbnormální počátek plicní arterie
ukАномальне відходження легеневої артерії
zh肺动脉起源异常
trPulmoner arterin anormal kökeni
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-11LA8B.1Especificvalidated
MONDO0015239Evalidated
MONDO15239Evalidated
UMLSC0265912Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

Children (3):

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card