ORPHA:98918
Acute motor axonal neuropathy
Synonyms: AMAN · Acute pure motor GBS · Acute pure motor Guillain-Barré syndrome
- Type
- Disease
- Group
- Disorder
- Inheritance
- Multigenic/multifactorial, Not applicable
- Age of onset
- All ages
- Status
- active
A rare pure motor axonal form of Guillain-Barré syndrome (GBS).
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Acute motor axonal neuropathy | AMAN · Acute pure motor GBS · Acute pure motor Guillain-Barré syndrome |
| fr | Neuropathie axonale motrice aiguë | AMAN · SGB moteur pur · Syndrome de Guillain-Barré moteur pur |
| de | Neuropathie, akute axonale motorische | AMAN · Guillain-Barré-Syndrom, akutes, rein motorisches |
| es | Neuropatía axonal motora aguda | GBS puro motor agudo · Síndrome de Guillain-Barré puro motor agudo |
| it | Neuropatia assonale motoria acuta | AMAN · GBS motoria pura acuta · Sindrome di Guillain-Barré motoria pura acuta |
| nl | Acute motorische axonale neuropathie | AMAN · Acuut zuiver motorisch GBS · Acuut zuiver motorisch syndroom van Guillain-Barré |
| pt | Neuropatia motora axonal, aguda (AMAN) | |
| pl | Ostra ruchowa neuropatia aksonalna | AMAN · Ostry czysty ruchowy GBS · Ostry czysty ruchowy zespół Guillaina i Barrégo |
| cs | Akutní motorická axonální neuropatie | AMAN · Akutní čistě motorický GBS · Akutní čistě motorický Guillainův-Barrého syndrom · Akutní čistě motorický Guillain-Barrého syndrom |
| uk | Гостра моторна аксональна нейропатія | Гострий чистий моторний GBS · Гострий чистий моторний синдром Гійєна-Барре · AMAN |
| zh | 急性运动轴突型神经病 | 急性单纯运动型吉兰巴雷综合征 |
| tr | Akut motor aksonal nöropati | AMAN · Akut saf motor GBS · Akut saf motor Guillain-Barré sendromu |
Definition in:
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | G61.0 | NTBT | attributed | validated |
| ICD-11 | 8C01.0 | NTBT | index | validated |
| MONDO | 0020349 | E | validated | |
| UMLS | C3890941 | E | validated | |
| MedDRA | 10076658 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:2103Guillain-Barré syndrome
rare neurological diseases
No children.
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Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
0 recordsNo prevalence record in this release.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/98918
- This record as JSON: /data/d/98918.json