{"orpha":98918,"name":"Acute motor axonal neuropathy","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["AMAN","Acute pure motor GBS","Acute pure motor Guillain-Barré syndrome"],"definition":"A rare pure motor axonal form of Guillain-Barré syndrome (GBS).","note":null,"url":"https://raremap.alftech.space/d/ORPHA-98918/","orphanet_url":"https://www.orpha.net/en/disease/detail/98918","names":{"fr":{"name":"Neuropathie axonale motrice aiguë","synonyms":["AMAN","SGB moteur pur","Syndrome de Guillain-Barré moteur pur"],"definition":"La neuropathie axonale motrice aiguë (AMAN) est une forme axonale, motrice pure, du syndrome de Guillain-Barré (SGB)."},"de":{"name":"Neuropathie, akute axonale motorische","synonyms":["AMAN","Guillain-Barré-Syndrom, akutes, rein motorisches"],"definition":"Die Akute motorische axonale Neuropathie (AMAN) ist ein rein motorische, axonale Form des Guillain-Barré-Syndroms (GBS; s. dort)."},"es":{"name":"Neuropatía axonal motora aguda","synonyms":["GBS puro motor agudo","Síndrome de Guillain-Barré puro motor agudo"],"definition":"Es una forma axonal motora pura del síndrome de Guillain-Barré (SGB)."},"it":{"name":"Neuropatia assonale motoria acuta","synonyms":["AMAN","GBS motoria pura acuta","Sindrome di Guillain-Barré motoria pura acuta"]},"nl":{"name":"Acute motorische axonale neuropathie","synonyms":["AMAN","Acuut zuiver motorisch GBS","Acuut zuiver motorisch syndroom van Guillain-Barré"],"definition":"Een zeldzame, zuiver motorische, axonale vorm van syndroom van Guillain-Barré (GBS)."},"pt":{"name":"Neuropatia motora axonal, aguda (AMAN)","definition":"A neuropatia axonal motora aguda (AMAN) é uma forma pura motora axonal do síndrome de Guillain-Barré (GBS; ver este termo)."},"pl":{"name":"Ostra ruchowa neuropatia aksonalna","synonyms":["AMAN","Ostry czysty ruchowy GBS","Ostry czysty ruchowy zespół Guillaina i Barrégo"]},"cs":{"name":"Akutní motorická axonální neuropatie","synonyms":["AMAN","Akutní čistě motorický GBS","Akutní čistě motorický Guillainův-Barrého syndrom","Akutní čistě motorický Guillain-Barrého syndrom"]},"uk":{"name":"Гостра моторна аксональна нейропатія","synonyms":["Гострий чистий моторний GBS","Гострий чистий моторний синдром Гійєна-Барре","AMAN"],"definition":"A rare pure motor axonal form of Guillain-Barré syndrome (GBS)."},"zh":{"name":"急性运动轴突型神经病","synonyms":["急性单纯运动型吉兰巴雷综合征"],"definition":"一种罕见的单纯运动性轴索形式的吉兰-巴雷综合征(GBS)。"},"tr":{"name":"Akut motor aksonal nöropati","synonyms":["AMAN","Akut saf motor GBS","Akut saf motor Guillain-Barré sendromu"]}},"xrefs":[{"source":"ICD-10","code":"G61.0","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"8C01.0","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"745197078"},{"source":"MONDO","code":"0020349","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C3890941","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10076658","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98006,"name":"Rare neurologic disease"},"parents":[{"orpha":2103,"name":"Guillain-Barré syndrome","classifications":[181]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Multigenic/multifactorial","Not applicable"],"onset":["All ages"],"prevalence":[],"phenotypes":null}