Guillain-Barré syndrome
Synonyms: GBS · Guillain-Barré-Strohl syndrome
- Type
- Clinical group
- Group
- Group of disorders
- Inheritance
- Multigenic/multifactorial
- Age of onset
- All ages
- Status
- active
A clinically heterogeneous spectrum of rare post-infectious neuropathies that usually occur in otherwise healthy patients and encompasses acute inflammatory demyelinating polyradiculoneuropathy (AIDP), acute motor axonal neuropathy (AMAN) and acute motor-sensory axonal neuropathy (AMSAN), Miller-Fisher syndrome (MFS) and some other regional variants.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Guillain-Barré syndrome | GBS · Guillain-Barré-Strohl syndrome |
| fr | Syndrome de Guillain-Barré | SGB · Syndrome de Guillain-Barré-Strohl |
| de | Guillain-Barré-Syndrom | GBS · Guillain-Barré-Strohl-Syndrom |
| es | Síndrome de Guillain-Barré | GBS · SGB · Síndrome de Guillain-Barré-Strohl |
| it | Sindrome di Guillain-Barré | GBS · Sindrome di Guillain-Barre · Sindrome di Guillain-Barré-Strohl |
| nl | Syndroom van Guillain-Barré | GBS · Syndroom van Guillain-Barré-Strohl |
| pt | Síndrome Guillain-Barré | |
| pl | Zespół Guillaina i Barrégo | GBS · Zespół Guillaina, Barrégo i Strohla |
| cs | Guillainův-Barrého syndrom | GBS · AIDP · Guillainův-Barrého-Strohlův syndrom · Landryho-Guillainův-Barrého syndrom · Guillain-Barrého syndrom · Guillain-Barrého-Strohlův syndrom · Landry-Guillain-Barrého syndrom |
| uk | Синдром Гієна-Барре | GBS · Синдром Гійєна-Барре-Строля |
| zh | 吉兰巴雷综合征 | Guillain-Barré-Strohl综合征 |
| tr | Guillain-Barre sendromu | GBS · Guillain-Barré-Strohl sendromu |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | G61.0 | E | specific | validated |
| ICD-11 | 8C01.0 | NTBT | index | validated |
| MONDO | 0016218 | E | validated | |
| MONDO | 16218 | E | validated | |
| MeSH | D020275 | E | validated | |
| UMLS | C0018378 | E | validated | |
| GARD | 6554 | E | validated | |
| MedDRA | 10018767 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (2):
- ORPHA:207038Acute and subacute inflammatory demyelinating polyneuropathy
rare neurological diseases - ORPHA:182064Rare neuroinflammatory or neuroimmunological disease
rare neurological diseases
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
7 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | 1-9 / 100 000 | 1.45 / 100 000 | Worldwide | Value and class | Validated | 19088488[PMID]_[EXPERT]_ ORPHANET |
| Annual incidence | 1-9 / 100 000 | 1.72 / 100 000 | United States | Value and class | Validated | 22846726[PMID] |
| Point prevalence | 1-9 / 100 000 | 3.5 / 100 000 | Europe | Value and class | Validated | [EXPERT]_European Medicines Agency 2007[OTHER]_ ORPHANET |
| Point prevalence | 1-5 / 10 000 | 25 / 100 000 | Denmark | Value and class | Validated | 20066507[PMID] |
| Annual incidence | 1-9 / 100 000 | 1.4 / 100 000 | Europe | Value and class | Not yet validated | 22694000[PMID]_ORPHANET |
| Point prevalence | 1-5 / 10 000 | 12 / 100 000 | Egypt | Value and class | Validated | 23146298[PMID] |
| Annual incidence | 1-9 / 100 000 | 2.42 / 100 000 | France | Value and class | Validated | 27991707[PMID] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/2103
- This record as JSON: /data/d/2103.json