ORPHA:98482
Idiopathic inflammatory myopathy
Synonyms: IMM · Idiopathic inflammatory myositis
- Type
- Category
- Group
- Group of disorders
- Status
- active
This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Idiopathic inflammatory myopathy | IMM · Idiopathic inflammatory myositis |
| fr | Myopathie inflammatoire idiopathique | IMM · MII · Myosite inflammatoire idiopathique |
| de | Myopathie, idiopathische inflammatorische | IMM · Myositis, idiopathische inflammatorische |
| es | Miopatía inflamatoria idiopática | IMM · Miositis inflamatoria idiopática |
| it | Miopatia infiammatoria idiopatica | IMM |
| nl | Idiopathische inflammatoire myopathie | IMM · Idiopathische inflammatoire myositis |
| pt | Miopatia e fasciite inflamatórias adquiridas | |
| pl | Idiopatyczna miopatia zapalna | IMM · Idiopatyczne zapalenie mięśni |
| cs | Idiopatické inflamatorní myopatie | IMM · Dysimunní myopatie |
| uk | Ідіопатична запальна міопатія | Ідіопатичний запальний міозит · IMM |
| zh | 特发性炎症肌病 | 特发性炎性肌炎 |
| tr | İdiyopatik inflamatuar miyopati | İBB · İdiyopatik inflamatuar miyozit |
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-11 | 4A41 | E | specific | validated |
| UMLS | C0751356 | E | validated | |
| GARD | 9128 | E | validated | |
| MedDRA | 10085970 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (2):
- ORPHA:206638Acquired skeletal muscle disease
rare neurological diseases - ORPHA:182228Systemic autoimmune disease
rare systemic and rheumatological diseases
Children (11):
- ORPHA:81Antisynthetase syndrome
- ORPHA:221Dermatomyositis
- ORPHA:3165Eosinophilic fasciitis
- ORPHA:48918Focal myositis
- ORPHA:247724Idiopathic eosinophilic myositis
- ORPHA:206569Immune-mediated necrotizing myopathy
- ORPHA:611Inclusion body myositis
- ORPHA:247718Inflammatory myopathy with abundant macrophages
- ORPHA:329888Juvenile idiopathic inflammatory myopathy
- ORPHA:206572Overlap myositis
- ORPHA:732Polymyositis
Codes that Orphanet moved or referred to this one:
- ORPHA:206979OBSOLETE: Granulomatous myositis referred to · inactive
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Validated | ORPHANET_30073460[PMID] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/98482
- This record as JSON: /data/d/98482.json