{"orpha":91140,"name":"Unspecified juvenile idiopathic arthritis","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Unspecified JIA"],"definition":"Unspecified juvenile idiopathic arthritis is a rare, pediatric, rheumatologic disease, a subtype of juvenile idiopathic arthritis (JIA) characterized by arthritis of an unknown cause that persists for at least 6 weeks, and does not fulfill the criteria for any of the other JIA subtypes, or fulfills criteria for more than one of the other subtypes.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-91140/","orphanet_url":"https://www.orpha.net/en/disease/detail/91140","names":{"fr":{"name":"Arthrite juvénile idiopathique indéterminée","synonyms":["AJI indéterminée"],"definition":"Maladie rhumatologique rare, pédiatrique, un sous-type d'arthrite juvénile idiopathique (AJI) caractérisé par une arthrite de cause inconnue persistant pendant au moins 6 semaines et ne répondant aux critères d'aucun autre sous-type ou répondant aux critères de plus d'un autre sous-type d'AJI."},"de":{"name":"Arthritis, idiopathische juvenile, unklassifizierte","synonyms":["Undifferenzierte JIA"]},"es":{"name":"Artritis idiopática juvenil no específica","synonyms":["AIJ no específica"],"definition":"Es una enfermedad reumatológica, pediátrica, poco frecuente, un subtipo de artritis idiopática juvenil (AIJ) caracterizada por artritis de causa desconocida que persiste durante al menos 6 semanas y no cumple con ningún criterio de los otros subtipos de AIJ, o cumple con más de un criterio de los otros subtipos."},"it":{"name":"Artrite idiopatica giovanile aspecifica","definition":"L'artrite idiopatica giovanile aspecifica è una malattia reumatica pediatrica rara consistente in un sottotipo dell'artrite idiopatica giovanile (AIG), caratterizzato da un'artrite ad eziologia non nota, che persiste per almeno sei settimane e non risponde ai criteri di nessun altro sottotipo di AIG, oppure risponde ai criteri di più sottotipi."},"nl":{"name":"Niet-gespecificeerde juveniele idiopathische artritis","synonyms":["Niet-gespecificeerde JIA"],"definition":"Niet-gespecificeerde juveniele idiopathische artritis is een zeldzame, pediatrische, reumatologische ziekte en een subtype van juveniele idiopathische artritis (JIA) dat gekarakteriseerd wordt door artritis met een onbekende oorzaak die minstens 6 weken aanhoudt, en dat niet voldoet aan de criteria van enig ander subtype van JIA, of voldoet aan criteria van meer dan een van de overige subtypes."},"pt":{"name":"Artrite idiopática juvenil, não-classificada"},"pl":{"name":"Niespecyficzne młodzieńcze idiopatyczne zapalenie stawów","synonyms":["Niespecyficzne JIA"],"definition":"*Niespecyficzne młodzieńcze idiopatyczne zapalenie stawów jest rzadką chorobą reumatologiczną dzieci, stanowi podtyp młodzieńczego idiopatycznego zapalenia stawów (ang. Juvenile Idiopathic Arthritis, JIA). Charakteryzuje się zapaleniem stawów o nieznanej przyczynie, które utrzymuje się przez co najmniej 6 tygodni i nie spełnia kryteriów żadnego z pozostałych podtypów JIA lub spełnia kryteria więcej niż jednego z pozostałych podtypów."},"cs":{"name":"Neklasifikovaná juvenilní idiopatická artritida","synonyms":["Unspecified JIA"]},"uk":{"name":"Неуточнений ювенільний ідіопатичний артрит","synonyms":["Невизначений JIA"],"definition":"Unspecified juvenile idiopathic arthritis is a rare, pediatric, rheumatologic disease, a subtype of juvenile idiopathic arthritis (JIA) characterized by arthritis of an unknown cause that persists for at least 6 weeks, and does not fulfill the criteria for any of the other JIA subtypes, or fulfills criteria for more than one of the other subtypes."},"zh":{"name":"不明青少年特发性关节炎","synonyms":["不明青少年特发性关节炎"]},"tr":{"name":"Tanımlanmamış juvenil idiyopatik artrit","synonyms":["Tanımlanmamış JIA"]}},"xrefs":[{"source":"ICD-10","code":"M08.8","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"FA24.Y","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"MONDO","code":"0019607","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5680196","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98023,"name":"Rare systemic or rheumatologic disease"},"parents":[{"orpha":92,"name":"Juvenile idiopathic arthritis","classifications":[184,196,231,233]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["Childhood","Infancy"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":null}