Myopericytoma
- Type
- Disease
- Group
- Disorder
- Status
- active
A rare soft tissue tumor characterized by a benign subcutaneous lesion composed of oval-to-spindle shaped myoid appearing cells with a tendency for concentric perivascular growth. The tumor usually presents as a painless, slowly growing nodule, which may be solitary or appear as multiple lesions, which then arise metachronously and usually involve a particular anatomic region. Recurrence after surgical excision may occur in poorly circumscribed tumors. Malignancy is very rare.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Myopericytoma | |
| fr | Myopéricytome | |
| de | Myoperizytom | |
| es | Miopericitoma | |
| it | Miopericitoma | |
| nl | Myopericytoom | |
| pt | Miopericitoma | |
| pl | Miopericytoma | |
| cs | Myopericytom | |
| uk | Міоперицитома | |
| zh | 肌周细胞瘤 | |
| tr | Miyoperisitom |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | D21.9 | NTBT | attributed | validated |
| MONDO | 0017349 | E | validated | |
| MeSH | D000077777 | E | validated | |
| UMLS | C1302808 | E | validated | |
| MedDRA | 10083440 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (2):
- ORPHA:289656Epstein-Barr Virus-associated mesenchymal tumor
rare neoplastic diseases - ORPHA:71209Rare soft tissue tumor
rare neoplastic diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/289685
- This record as JSON: /data/d/289685.json