raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:700133

Idiopathic chronic pancreatitis

Type
Disease
Group
Disorder
Inheritance
Not applicable
Age of onset
Adolescent, Adult, Childhood
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

9 of 12 languages
LangNameSynonyms
enIdiopathic chronic pancreatitis
frPancréatite chronique idiopathique
dePankreatitis, chronische idiopathische
esPancreatitis crónica idiopática
itPancreatite cronica idiopatica
nlIdiopathische chronische pancreatitisIdiopathische chronische alvleesklierontsteking
ptIdiopathic chronic pancreatitis
plIdiopathic chronic pancreatitis
csIdiopathic chronic pancreatitis
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10K86.1NTBTattributednot yet validated
ICD-11DC32.4Especificvalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

Children (2):

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

1 record
TypeClassValueAreaQualificationValidationSource
Point prevalence1-5 / 10 00012.5 / 100 000WorldwideValue and classValidatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card