{"orpha":700133,"name":"Idiopathic chronic pancreatitis","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":[],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-700133/","orphanet_url":"https://www.orpha.net/en/disease/detail/700133","names":{"fr":{"name":"Pancréatite chronique idiopathique"},"de":{"name":"Pankreatitis, chronische idiopathische"},"es":{"name":"Pancreatitis crónica idiopática"},"it":{"name":"Pancreatite cronica idiopatica"},"nl":{"name":"Idiopathische chronische pancreatitis","synonyms":["Idiopathische chronische alvleesklierontsteking"]},"pt":{"name":"Idiopathic chronic pancreatitis"},"pl":{"name":"Idiopathic chronic pancreatitis"},"cs":{"name":"Idiopathic chronic pancreatitis"}},"xrefs":[{"source":"ICD-10","code":"K86.1","qualifier":"NTBT","icd_relation":"attributed","validated":false},{"source":"ICD-11","code":"DC32.4","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"220806888"}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":97935,"name":"Rare gastroenterologic disease"},"parents":[{"orpha":101937,"name":"Rare pancreatic disease","classifications":[152]}],"children":[{"orpha":700136,"name":"Early-onset idiopathic chronic pancreatitis","type":"Clinical subtype"},{"orpha":700139,"name":"Late-onset idiopathic chronic pancreatitis","type":"Clinical subtype"}],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adolescent","Adult","Childhood"],"prevalence":[{"type":"Point prevalence","qualification":"Value and class","class":"1-5 / 10 000","value":12.5,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":null}