raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:700136

Early-onset idiopathic chronic pancreatitis

Type
Clinical subtype
Group
Subtype of disorder
Inheritance
Not applicable
Age of onset
Adolescent, Adult
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

9 of 12 languages
LangNameSynonyms
enEarly-onset idiopathic chronic pancreatitis
frPancréatite chronique idiopathique précoce
dePankreatitis, chronische idiopathische, früh beginnende
esPancreatitis crónica idiopática de inicio precoz
itPancreatite cronica idiopatica ad esordio precoce
nlVroeg optredende idiopathische chronische pancreatitisVroeg optredende idiopathische chronische alvleesklierontsteking
ptEarly-onset idiopathic chronic pancreatitis
plEarly-onset idiopathic chronic pancreatitis
csEarly-onset idiopathic chronic pancreatitis
2

Cross-references

qualifier = Orphanet mapping relation

No cross-references in this release.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

1 record
TypeClassValueAreaQualificationValidationSource
Point prevalence1-9 / 100 0006 / 100 000WorldwideValue and classValidatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card