raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:658574

Isolated pulmonary artery sling

Synonyms: Isolated anomalous left pulmonary artery · Isolated left pulmonary artery sling · LPA · PAS

Type
Morphological anomaly
Group
Disorder
Inheritance
Not applicable
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

10 of 12 languages
LangNameSynonyms
enIsolated pulmonary artery slingIsolated anomalous left pulmonary artery · Isolated left pulmonary artery sling · LPA · PAS
frArtère pulmonaire gauche rétro-trachéaleAnomalie isolée rétrotrachéale de l'artère pulmonaire gauche · Artère pulmonaire gauche rétrotrachéale
dePulmonalisschlinge, isolierteIsolierte anomale linke Pulmonalarterie · Isolierte pulmonalarterielle Schlinge · PAS
esSling aislado de la arteria pulmonarArteria pulmonar izquierda aberrante aislada · Asa aislada de la arteria pulmonar · Cabestrillo aislado de la arteria pulmonar · SAP · Sling aislado de la arteria pulmonar izquierda · Sling aislado pulmonar
itArteria polmonare aberrante isolataArteria polmonare sinistra anomala isolata · LPA · PAS · Arteria polmonare sinistra aberrante isolata
nlGeïsoleerde sling van arteria pulmonalisGeïsoleerde abnormale oorsprong van linker longslagader · Geïsoleerde afwijkende linker longarterie · LPA · PAS
ptFunda isolada da artéria pulmonarArtéria pulmonar esquerda anómala isolada · Funda isolada da artéria pulmonar esquerda · LPA · PAS
plIzolowana pętla tętnicy płucnej= en
csIzolovaná pulmonální smyčka= en
ukІзольований бандаж легеневої артеріїІзольована аномальна ліва легенева артерія · Ізольована перевязка лівої легеневої артерії · LPA · PAS
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10Q25.7NTBTattributedvalidated
ICD-11LA8B.YNTBTindexvalidated
MONDO0958123Evalidated
MONDO958123Evalidated
UMLSC1856123Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card