ORPHA:658574
Isolated pulmonary artery sling
Synonyms: Isolated anomalous left pulmonary artery · Isolated left pulmonary artery sling · LPA · PAS
- Type
- Morphological anomaly
- Group
- Disorder
- Inheritance
- Not applicable
- Status
- active
Orphadata ships no English definition for this code.
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Names in Orphadata languages
10 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Isolated pulmonary artery sling | Isolated anomalous left pulmonary artery · Isolated left pulmonary artery sling · LPA · PAS |
| fr | Artère pulmonaire gauche rétro-trachéale | Anomalie isolée rétrotrachéale de l'artère pulmonaire gauche · Artère pulmonaire gauche rétrotrachéale |
| de | Pulmonalisschlinge, isolierte | Isolierte anomale linke Pulmonalarterie · Isolierte pulmonalarterielle Schlinge · PAS |
| es | Sling aislado de la arteria pulmonar | Arteria pulmonar izquierda aberrante aislada · Asa aislada de la arteria pulmonar · Cabestrillo aislado de la arteria pulmonar · SAP · Sling aislado de la arteria pulmonar izquierda · Sling aislado pulmonar |
| it | Arteria polmonare aberrante isolata | Arteria polmonare sinistra anomala isolata · LPA · PAS · Arteria polmonare sinistra aberrante isolata |
| nl | Geïsoleerde sling van arteria pulmonalis | Geïsoleerde abnormale oorsprong van linker longslagader · Geïsoleerde afwijkende linker longarterie · LPA · PAS |
| pt | Funda isolada da artéria pulmonar | Artéria pulmonar esquerda anómala isolada · Funda isolada da artéria pulmonar esquerda · LPA · PAS |
| pl | Izolowana pętla tętnicy płucnej | = en |
| cs | Izolovaná pulmonální smyčka | = en |
| uk | Ізольований бандаж легеневої артерії | Ізольована аномальна ліва легенева артерія · Ізольована перевязка лівої легеневої артерії · LPA · PAS |
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | Q25.7 | NTBT | attributed | validated |
| ICD-11 | LA8B.Y | NTBT | index | validated |
| MONDO | 0958123 | E | validated | |
| MONDO | 958123 | E | validated | |
| UMLS | C1856123 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
3
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:1138Abnormal origin of the pulmonary artery
rare developmental anomalies during embryogenesis; rare cardiac malformations
No children.
4
Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
0 recordsNo prevalence record in this release.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/658574
- This record as JSON: /data/d/658574.json