{"orpha":658574,"name":"Isolated pulmonary artery sling","type":"Morphological anomaly","group":"Disorder","status":"active","flags":[],"synonyms":["Isolated anomalous left pulmonary artery","Isolated left pulmonary artery sling","LPA","PAS"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-658574/","orphanet_url":"https://www.orpha.net/en/disease/detail/658574","names":{"fr":{"name":"Artère pulmonaire gauche rétro-trachéale","synonyms":["Anomalie isolée rétrotrachéale de l'artère pulmonaire gauche","Artère pulmonaire gauche rétrotrachéale"]},"de":{"name":"Pulmonalisschlinge, isolierte","synonyms":["Isolierte anomale linke Pulmonalarterie","Isolierte pulmonalarterielle Schlinge","PAS"]},"es":{"name":"Sling aislado de la arteria pulmonar","synonyms":["Arteria pulmonar izquierda aberrante aislada","Asa aislada de la arteria pulmonar","Cabestrillo aislado de la arteria pulmonar","SAP","Sling aislado de la arteria pulmonar izquierda","Sling aislado pulmonar"]},"it":{"name":"Arteria polmonare aberrante isolata","synonyms":["Arteria polmonare sinistra anomala isolata","LPA","PAS","Arteria polmonare sinistra aberrante isolata"]},"nl":{"name":"Geïsoleerde sling van arteria pulmonalis","synonyms":["Geïsoleerde abnormale oorsprong van linker longslagader","Geïsoleerde afwijkende linker longarterie","LPA","PAS"]},"pt":{"name":"Funda isolada da artéria pulmonar","synonyms":["Artéria pulmonar esquerda anómala isolada","Funda isolada da artéria pulmonar esquerda","LPA","PAS"]},"pl":{"name":"Izolowana pętla tętnicy płucnej","synonyms":["Isolated anomalous left pulmonary artery","Isolated left pulmonary artery sling","LPA","PAS"]},"cs":{"name":"Izolovaná pulmonální smyčka","synonyms":["Isolated anomalous left pulmonary artery","Isolated left pulmonary artery sling","LPA","PAS"]},"uk":{"name":"Ізольований бандаж легеневої артерії","synonyms":["Ізольована аномальна ліва легенева артерія","Ізольована перевязка лівої легеневої артерії","LPA","PAS"]}},"xrefs":[{"source":"ICD-10","code":"Q25.7","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"LA8B.Y","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"1038861606"},{"source":"MONDO","code":"0958123","qualifier":"E","icd_relation":null,"validated":true},{"source":"MONDO","code":"958123","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C1856123","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":93890,"name":"Rare developmental defect during embryogenesis"},"parents":[{"orpha":1138,"name":"Abnormal origin of the pulmonary artery","classifications":[147,148]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":[],"prevalence":[],"phenotypes":null}