ORPHA:56044
Carcinoma of gallbladder and extrahepatic biliary tract
Synonyms: Carcinoma of gallbladder and EBT
- Type
- Clinical group
- Group
- Group of disorders
- Inheritance
- Not applicable
- Age of onset
- Adult
- Status
- active
Carcinoma of the gallbladder (GBC) is the most common and aggressive form of biliary tract cancer (BTC) usually arising in the fundus of the gallbladder, rapidly metastasizing to lymph nodes and distant sites.
1
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Carcinoma of gallbladder and extrahepatic biliary tract | Carcinoma of gallbladder and EBT |
| fr | Carcinome de la vésicule biliaire et des voies biliaires extrahépatiques | Carcinome de la vésicule biliaire et des VBEH |
| de | Karzinom der Gallenblase und der extrahepatischen Gallengänge | GBC · Gallenblasen- und EBT-Karzinom |
| es | Carcinoma de vesícula y vías biliares extrahepáticas | Carcinoma de vesícula y VBE · GBC |
| it | Carcinoma della cistifellea e delle vie biliari extraepatiche | Carcinoma della cistifellea e delle VBE · GBC |
| nl | Carcinoom van galblaas en extrahepatische galwegen | Carcinoom van galblaas en EBT · GBC |
| pt | Carcinoma da vesícula biliar | |
| pl | Rak pęchrzyka żółciowego i zewnątrzwątrobowych przewodów żółciowych | GBC · Rak pęchrzyka żółciowego i EBT |
| cs | Karcinom žlučníku a extrahepatických žlučových cest | Karcinom žlučníku a EBT |
| uk | Карцинома жовчного міхура та позапечінкових жовчовивідних шляхів | Карцинома жовчного міхура та ЕБТ |
| zh | 胆囊癌和肝外胆管癌 | 胆囊癌和EBT癌 |
| tr | Safra kesesi karsinomu ve ekstrahepatik safra yolları | Safra kesesi karsinomu ve EBT |
Definition in:
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| MONDO | 0018918 | E | validated | |
| MONDO | 18918 | E | validated | |
| UMLS | C5566557 | E | validated | |
| MedDRA | 10007426 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:306633Rare tumor of gallbladder and extrahepatic biliary tract
rare hepatic diseases; rare neoplastic diseases
Children (5):
4
Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
7 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | 1-5 / 10 000 | 12 / 100 000 | Worldwide | Value and class | Validated | ORPHANET |
| Annual incidence | 1-9 / 100 000 | 5.3 / 100 000 | Japan | Value and class | Not yet validated | ORPHANET |
| Annual incidence | 1-9 / 100 000 | 1.5 / 100 000 | United States | Value and class | Not yet validated | 13835134[PMID]_17857545[PMID]_13425293[PMID]_22570746[PMID] |
| Annual incidence | 1-5 / 10 000 | 14 / 100 000 | Poland | Value and class | Validated | 16397865[PMID] |
| Annual incidence | 1-9 / 100 000 | 1.27 / 100 000 | France | Value and class | Not yet validated | 10951337[PMID] |
| Point prevalence | 1-5 / 10 000 | — | Europe | Class only | Not yet validated | ORPHANET |
| Annual incidence | 1-9 / 100 000 | 4.37 / 100 000 | Europe | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/56044
- This record as JSON: /data/d/56044.json