Adenocarcinoma of the gallbladder and extrahepatic biliary tract
Synonyms: Adenocarcinoma of the gallbladder and EBT
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adult
- Status
- active
A rare epithelial carcinoma, arising either in the gallbladder itself or from the epithelium lining the extrahepatic biliary tree, cystic duct and/or peribiliary gland, characterized by nonspecific symptoms, such as abdominal pain, jaundice and vomiting and sometimes mimicking benign biliary diseases. Chronic biliary epithelial inflammation (e.g. primary sclerosing cholangitis, cholelithiasis, choledocholithiasis, liver fluke infestation) is a major risk factor.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Adenocarcinoma of the gallbladder and extrahepatic biliary tract | Adenocarcinoma of the gallbladder and EBT |
| fr | Adénocarcinome de la vésicule biliaire et des voies biliaires extrahépatiques | Adénocarcinome de la vésicule biliaire et des VBEH |
| de | Adenokarzinom der Gallenblase und extrahepatischen Gallengänge | Adenokarzinom der Gallenblase und EBT |
| es | Adenocarcinoma de la vesícula biliar y de las vías biliares extrahepáticas | Adenocarcinoma de vesícula y VBE |
| it | Adenocarcinoma della cistifellea e delle vie biliari extraepatiche | Adenocarcinoma della cistifellea e delle VBE |
| nl | Adenocarcinoom van galblaas en extrahepatische galwegen | Adenocarcinoom van galblaas en EBT |
| pt | Adenocarcinoma da vesícula biliar e do trato biliar extra-hepático | Adenocarcinoma da vesícula biliar e do TBEH |
| pl | Gruczolakorak pęcherzyka żółciowego i zewnątrzwątrobowego przewodu żółciowego | Gruczolakorak pęcherzyka żółciowego i EBT |
| cs | Adenokarcinom žlučníku a extrahepatálních žlučových cest | Adenokarcinom žlučníku a EBT |
| uk | Аденокарцинома жовчного міхура та позапечінкових жовчовивідних шляхів | Аденокарцинома жовчного міхура та EBT |
| zh | 胆囊和肝外胆道腺癌 | 胆囊腺癌和EBT |
| tr | Safra kesesi adenokarsinomu ve ekstrahepatik safra yolları | Safra kesesi adenokarsinomu ve EBT |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C23 | BTNT | attributed | validated |
| ICD-10 | C24.0 | BTNT | attributed | validated |
| ICD-10 | C24.1 | BTNT | attributed | validated |
| ICD-10 | C24.8 | BTNT | attributed | validated |
| MONDO | 0018536 | E | validated | |
| UMLS | C4707555 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:56044Carcinoma of gallbladder and extrahepatic biliary tract
rare hepatic diseases; rare neoplastic diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | 1-9 / 100 000 | 2.62 / 100 000 | Europe | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/424991
- This record as JSON: /data/d/424991.json