raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:506052

Neuroendocrine neoplasm of pancreas

Synonyms: PNEN · Pancreatic NEN · Pancreatic neuroendocrine neoplasm

Type
Category
Group
Group of disorders
Status
active

This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enNeuroendocrine neoplasm of pancreasPNEN · Pancreatic NEN · Pancreatic neuroendocrine neoplasm
frNéoplasme neuroendocrine du pancréasNeoplasm neuroendocrine pancréatique · PNEN
deNeuroendokrine Neoplasie des PankreasPNEN · PNET
esNeoplasia neuroendocrina de páncreasNEN pancreática · Neoplasia neuroendocrina pancreática · PNEN
itNeoplasia neuroendocrina del pancreas
nlNeuro-endocrien neoplasma van pancreasNeuro-endocrien neoplasma van alvleesklier · PNEN · Pancreatisch NEN · Pancreatisch neuro-endocrien neoplasma
ptNeoplasia neuroendócrina do pâncreas
plNowotwór neuroendokrynny trzustki= en
csNeuroendokrinní novotvar pankreatuPNEN · Pankreatický NEN · Pankreatický neuroendokrinní novotvar
ukНейроендокринна пухлина підшлункової залозиNEN підшлункової залози · Нейроендокринна пухлина підшлункової залози · PNEN
zh胰腺神经内分泌肿瘤= en
trPankreasın nöroendokrin neoplazmıPNEN · Pankreatik NEN · Pankreatik nöroendokrin neoplazmı
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-112C10.1Especificvalidated
MONDO0005815Evalidated
MONDO5815Evalidated
UMLSC5848399Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (2):

Children (3):

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card