ORPHA:506052
Neuroendocrine neoplasm of pancreas
Synonyms: PNEN · Pancreatic NEN · Pancreatic neuroendocrine neoplasm
- Type
- Category
- Group
- Group of disorders
- Status
- active
This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.
1
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Neuroendocrine neoplasm of pancreas | PNEN · Pancreatic NEN · Pancreatic neuroendocrine neoplasm |
| fr | Néoplasme neuroendocrine du pancréas | Neoplasm neuroendocrine pancréatique · PNEN |
| de | Neuroendokrine Neoplasie des Pankreas | PNEN · PNET |
| es | Neoplasia neuroendocrina de páncreas | NEN pancreática · Neoplasia neuroendocrina pancreática · PNEN |
| it | Neoplasia neuroendocrina del pancreas | |
| nl | Neuro-endocrien neoplasma van pancreas | Neuro-endocrien neoplasma van alvleesklier · PNEN · Pancreatisch NEN · Pancreatisch neuro-endocrien neoplasma |
| pt | Neoplasia neuroendócrina do pâncreas | |
| pl | Nowotwór neuroendokrynny trzustki | = en |
| cs | Neuroendokrinní novotvar pankreatu | PNEN · Pankreatický NEN · Pankreatický neuroendokrinní novotvar |
| uk | Нейроендокринна пухлина підшлункової залози | NEN підшлункової залози · Нейроендокринна пухлина підшлункової залози · PNEN |
| zh | 胰腺神经内分泌肿瘤 | = en |
| tr | Pankreasın nöroendokrin neoplazmı | PNEN · Pankreatik NEN · Pankreatik nöroendokrin neoplazmı |
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-11 | 2C10.1 | E | specific | validated |
| MONDO | 0005815 | E | validated | |
| MONDO | 5815 | E | validated | |
| UMLS | C5848399 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (2):
- ORPHA:100092Gastroenteropancreatic neuroendocrine neoplasm
rare endocrine diseases; rare neoplastic diseases - ORPHA:424033Rare epithelial tumor of pancreas
rare gastroenterological diseases; rare neoplastic diseases
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Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
0 recordsNo prevalence record in this release.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/506052
- This record as JSON: /data/d/506052.json