Mixed neuroendocrine and non-neuroendocrine neoplasm of pancreas
Synonyms: MiNEN of pancreas · Pancreatic MiNEN · Pancreatic mixed neuroendocrine-nonneuroendocrine neoplasm
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Status
- active
A rare neuroendocrine neoplasm of pancreas characterized by morphologically recognizable neuroendocrine and non-neuroendocrine components, each constituting at least 30% of the tumor volume. Based on histopathology, mixed ductal- and mixed acinar-neuroendocrine carcinomas are distinguished. Patients usually present with unspecific symptoms related to tumor growth and/or metastasis, although occurrence of Zollinger-Ellison syndrome has been reported. Resectability of the tumor is the most important prognostic factor.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Mixed neuroendocrine and non-neuroendocrine neoplasm of pancreas | MiNEN of pancreas · Pancreatic MiNEN · Pancreatic mixed neuroendocrine-nonneuroendocrine neoplasm |
| fr | Néoplasme neuroendocrine-non neuroendocrine mixte du pancréas | MiNEN · MiNEN du pancréas · MiNEN pancréatique · Néoplasme neuroendocrine-nonneuroendocrine mixte pancréatique |
| de | Gemischte neuroendokrine/nicht neuroendokrine Neoplasie des Pankreas | MiNEN des Pankreas · Pankreatische MiNEN · Pankreatische gemischte neuroendokrine-nicht-neuroendokrine Neoplasie |
| es | Neoplasia mixta neuroendocrina y no neuroendocrina de páncreas | MiNEN de páncreas · MiNEN pancreática · Neoplasia neuroendocrina y no neuroendocrina pancreática mixta |
| it | Neoplasia mista neuroendocrina-non neuroendocrina del pancreas | MiNEN del pancreas · MiNEN pancreatica · Neoplasia mista neuroendocrina-non neuroendocrina pancreatica |
| nl | Gemengd neuro-endocrien en niet-neuro-endocrien neoplasma van pancreas | Gemengd neuro-endocrien en niet-neuro-endocrien neoplasma van alvleesklier · MiNEN van pancreas · Pancreatisch MiNEN · Pancreatisch gemengd neuro-endocrien - niet-neuro-endocrien neoplasma |
| pt | Neoplasia neuroendócrina e não-neuroendócrina mista do pâncreas | |
| pl | Nowotwór trzustki mieszany neuroendokrynny i nie-neuroendokrynny | = en |
| cs | Smíšený neuroendokrinní a nonneuroendokrinní novotvar pankreatu | Pankreatický MiNEN · MiNEN pankreatu · Pankreatický smíšený neuroendokrinní a nonneuroendokrinní novotvar |
| uk | Змішана нейроендокринна та ненейроендокринна пухлина підшлункової залози | МіНен підшлункової залози · Підшлункова залоза MiNEN · Змішана нейроендокринно-нейроендокринна пухлина підшлункової залози |
| zh | 胰腺混合性神经内分泌-非神经内分泌肿瘤 | = en |
| tr | Pankreasın karma nöroendokrin-nöroendokrin olmayan neoplazmı | Pankreatik MiNEN · MiNEN pankreas · Pankreatik karma nöroendokrin-nöroendokrin olmayan neoplazm |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C25.9 | NTBT | attributed | validated |
| ICD-11 | 2C10.Y | NTBT | attributed | validated |
| MONDO | 0044727 | E | validated | |
| MONDO | 44727 | E | validated | |
| UMLS | C5568577 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:506052Neuroendocrine neoplasm of pancreas
rare gastroenterological diseases; rare endocrine diseases; rare neoplastic diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/506112
- This record as JSON: /data/d/506112.json