{"orpha":506052,"name":"Neuroendocrine neoplasm of pancreas","type":"Category","group":"Group of disorders","status":"active","flags":[],"synonyms":["PNEN","Pancreatic NEN","Pancreatic neuroendocrine neoplasm"],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-506052/","orphanet_url":"https://www.orpha.net/en/disease/detail/506052","names":{"fr":{"name":"Néoplasme neuroendocrine du pancréas","synonyms":["Neoplasm neuroendocrine pancréatique","PNEN"]},"de":{"name":"Neuroendokrine Neoplasie des Pankreas","synonyms":["PNEN","PNET"]},"es":{"name":"Neoplasia neuroendocrina de páncreas","synonyms":["NEN pancreática","Neoplasia neuroendocrina pancreática","PNEN"]},"it":{"name":"Neoplasia neuroendocrina del pancreas"},"nl":{"name":"Neuro-endocrien neoplasma van pancreas","synonyms":["Neuro-endocrien neoplasma van alvleesklier","PNEN","Pancreatisch NEN","Pancreatisch neuro-endocrien neoplasma"]},"pt":{"name":"Neoplasia neuroendócrina do pâncreas"},"pl":{"name":"Nowotwór neuroendokrynny trzustki","synonyms":["PNEN","Pancreatic NEN","Pancreatic neuroendocrine neoplasm"]},"cs":{"name":"Neuroendokrinní novotvar pankreatu","synonyms":["PNEN","Pankreatický NEN","Pankreatický neuroendokrinní novotvar"]},"uk":{"name":"Нейроендокринна пухлина підшлункової залози","synonyms":["NEN підшлункової залози","Нейроендокринна пухлина підшлункової залози","PNEN"]},"zh":{"name":"胰腺神经内分泌肿瘤","synonyms":["PNEN","Pancreatic NEN","Pancreatic neuroendocrine neoplasm"]},"tr":{"name":"Pankreasın nöroendokrin neoplazmı","synonyms":["PNEN","Pankreatik NEN","Pankreatik nöroendokrin neoplazmı"]}},"xrefs":[{"source":"ICD-11","code":"2C10.1","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"1421495979"},{"source":"MONDO","code":"0005815","qualifier":"E","icd_relation":null,"validated":true},{"source":"MONDO","code":"5815","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5848399","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":100092,"name":"Gastroenteropancreatic neuroendocrine neoplasm","classifications":[193,202]},{"orpha":424033,"name":"Rare epithelial tumor of pancreas","classifications":[152,202]}],"children":[{"orpha":506112,"name":"Mixed neuroendocrine and non-neuroendocrine neoplasm of pancreas","type":"Disease"},{"orpha":506098,"name":"Neuroendocrine carcinoma of pancreas","type":"Disease"},{"orpha":97253,"name":"Neuroendocrine tumor of pancreas","type":"Category"}],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}