{"orpha":439729,"name":"Cutaneous polyarteritis nodosa","type":"Clinical subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":["Cutaneous PAN","Cutaneous periarteritis nodosa"],"definition":"Cutaneous polyarteritis nodosa (CPAN) is a rare limited form of polyarteritis nodosa (PAN), characterized by cutaneous vasculitis and mild and transient extracutaneous manifestations such as mild arthralgia, arthritis,myalgia, and rarely peripheral neuropathy.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-439729/","orphanet_url":"https://www.orpha.net/en/disease/detail/439729","names":{"fr":{"name":"Périartérite noueuse cutanée","synonyms":["PAN cutanée","Polyartérite noueuse cutanée"],"definition":"Forme rare et limitée de périartérite noueuse, caractérisée par une vascularite cutanée et de légères manifestations extracutanées transitoires, telles qu'une arthralgie légère, une arthrite, une myalgie et, dans de rares cas, une neuropathie périphérique."},"de":{"name":"Kutane Polyarteriitis nodosa","synonyms":["Kutane PAN","Kutane Periarteriitis nodosa"]},"es":{"name":"Poliarteritis nodosa cutánea","synonyms":["PAN cutánea","Periarteritis nodosa cutánea"],"definition":"Es una forma restringida de poliarteritis nodosa (PAN, consulte este término) poco frecuente caracterizada por vasculitis cutánea y manifestaciones extracutáneas leves y transitorias, tales como leve artralgia, artritis, mialgia y, excepcionalmente, neuropatía periférica."},"it":{"name":"Poliarterite nodosa cutanea","synonyms":["PAN cutanea","Periarterite nodosa cutanea"],"definition":"La poliarterite nodosa cutanea (CPAN) è una forma rara e limitata di poliarterite nodosa (PAN; si veda questo termine), caratterizzata da vasculite cutanea e segni extracutanei lievi e transitori, come l'artralgia, l'artrite e la mialgia lievi e, raramente, la neuropatia periferica."},"nl":{"name":"Cutane polyarteriitis nodosa","synonyms":["Cutane PAN","Cutane periarteriitis nodosa"],"definition":"Cutane polyarteriitis nodosa (CPAN) is een zeldzame, beperkte vorm van polyarteriitis nodosa (PAN; zie deze term), die wordt gekarakteriseerd door cutane vasculitis en milde en transiënte extracutane manifestaties zoals milde artralgie, artritis, myalgie, en in zeldzame gevallen perifere neuropathie."},"pt":{"name":"Poliarterite nodosa cutânea"},"pl":{"name":"Skórne guzkowe zapalenie tętnic","synonyms":["Skórne PAN"]},"cs":{"name":"Kožní polyarteritis nodosa","synonyms":["Kožní PAN","Kožní periarteritis nodosa"]},"uk":{"name":"Вузликовий шкірний поліартеріїт","synonyms":["Шкірний PAN","Вузликовий шкірний періартеріїт"],"definition":"Cutaneous polyarteritis nodosa (CPAN) is a rare limited form of polyarteritis nodosa (PAN, see this term), characterized by cutaneous vasculitis and mild and transient extracutaneous manifestations such as mild arthralgia, arthritis,myalgia, and rarely peripheral neuropathy."},"zh":{"name":"皮肤结节性多动脉炎","synonyms":["皮肤结节性动脉周围炎"],"definition":"皮肤结节性多发性动脉炎（CPAN）是结节性多发性动脉炎（PAN，参见本术语）的一种罕见的形式，其特征是皮肤血管炎和轻度并短暂的皮外表现，例如轻度关节痛，关节炎，肌痛，罕见的周围神经病变。"},"tr":{"name":"Kutanöz poliarteritis nodoza","synonyms":["Kutanöz PAN","Kutanöz periarterit nodosa"]}},"xrefs":[{"source":"ICD-10","code":"M30.0","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"EF40.Z","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"1752423171"},{"source":"MONDO","code":"0018592","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0343190","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"7415","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98023,"name":"Rare systemic or rheumatologic disease"},"parents":[{"orpha":439737,"name":"Primary polyarteritis nodosa","classifications":[181,188,196,198,231,233]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":[],"prevalence":[],"phenotypes":null}