ORPHA:314970
Lymphocytic hypereosinophilic syndrome
Synonyms: HES-L · Lymphocytic variant HES · Lymphoid HES
- Type
- Clinical subtype
- Group
- Subtype of disorder
- Age of onset
- All ages
- Status
- active
Orphadata ships no English definition for this code.
1
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Lymphocytic hypereosinophilic syndrome | HES-L · Lymphocytic variant HES · Lymphoid HES |
| fr | Syndrome hyperéosinophilique lymphoïde | SHE variant lymphoïde · SHE-L |
| de | Hypereosinophiles Syndrom, lymphoides | HES, lymphoides · HES-L |
| es | Síndrome hipereosinofílico linfoide | HES linfoide · HES-L |
| it | Sindrome ipereosinofila linfoide | HES linfoide · HES-L |
| nl | Lymfoïd hypereosinofiel syndroom | HES-L · Lymfoïde HES |
| pt | Síndrome hipereosinofílico linfóide | HES Linfóide · HES-L |
| pl | Limfoidalny zespół hipereozynofilowy | HES-L · Limfoidalny HES |
| cs | Lymfocytární varianta hypereozinofilního syndromu | HES-L · Lymfocytární varianta HES · Lymfoidní HES |
| uk | Лімфоцитарний гіпереозинофільний синдром | HES-L · Лімфоцитарний варіант HES · Лімфоїдна HES |
| zh | 淋巴细胞性嗜酸性粒细胞增多综合征 | 淋巴细胞变异性HES |
| tr | Lenfositik hipereozinofilik sendrom | HES-L · Lenfoid HES · Lenfositik varyant HES |
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | D47.5 | NTBT | attributed | validated |
| ICD-11 | BC43.20 | NTBT | index | validated |
| MONDO | 0017835 | E | validated | |
| UMLS | C5396402 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
3
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:314962Secondary hypereosinophilic syndrome
rare cardiac diseases; rare hematological diseases; rare neoplastic diseases; rare transplant-related disorders
No children.
4
Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/314970
- This record as JSON: /data/d/314970.json