{"orpha":314970,"name":"Lymphocytic hypereosinophilic syndrome","type":"Clinical subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":["HES-L","Lymphocytic variant HES","Lymphoid HES"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-314970/","orphanet_url":"https://www.orpha.net/en/disease/detail/314970","names":{"fr":{"name":"Syndrome hyperéosinophilique lymphoïde","synonyms":["SHE variant lymphoïde","SHE-L"]},"de":{"name":"Hypereosinophiles Syndrom, lymphoides","synonyms":["HES, lymphoides","HES-L"]},"es":{"name":"Síndrome hipereosinofílico linfoide","synonyms":["HES linfoide","HES-L"]},"it":{"name":"Sindrome ipereosinofila linfoide","synonyms":["HES linfoide","HES-L"]},"nl":{"name":"Lymfoïd hypereosinofiel syndroom","synonyms":["HES-L","Lymfoïde HES"]},"pt":{"name":"Síndrome hipereosinofílico linfóide","synonyms":["HES Linfóide","HES-L"]},"pl":{"name":"Limfoidalny zespół hipereozynofilowy","synonyms":["HES-L","Limfoidalny HES"]},"cs":{"name":"Lymfocytární varianta hypereozinofilního syndromu","synonyms":["HES-L","Lymfocytární varianta HES","Lymfoidní HES"]},"uk":{"name":"Лімфоцитарний гіпереозинофільний синдром","synonyms":["HES-L","Лімфоцитарний варіант HES","Лімфоїдна HES"]},"zh":{"name":"淋巴细胞性嗜酸性粒细胞增多综合征","synonyms":["淋巴细胞变异性HES"]},"tr":{"name":"Lenfositik hipereozinofilik sendrom","synonyms":["HES-L","Lenfoid HES","Lenfositik varyant HES"]}},"xrefs":[{"source":"ICD-10","code":"D47.5","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"BC43.20","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"367714724"},{"source":"MONDO","code":"0017835","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5396402","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":97992,"name":"Rare hematologic disease"},"parents":[{"orpha":314962,"name":"Secondary hypereosinophilic syndrome","classifications":[146,194,202,233]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["All ages"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}